نتایج جستجو برای: small supernumerary marker chromosome ssmc

تعداد نتایج: 1015567  

Journal: :international journal of molecular and cellular medicine 0
javad karimzad hagh parseh pathobiology & genetics laboratory, tehran, iran. thomas liehr jena university hospital, friedrich schiller university, institute of human genetics, jena, germany. hamid ghaedi department of medical genetics, faculty of medicine, shahid beheshti university of medical sciences, tehran, iran. mir majid mossalaeie parseh pathobiology & genetics laboratory, tehran, iran. shohreh alimohammadi endometrium and endometriosis research center, faculty of medicine, hamedan university of medical sciences, hamedan, iran. faegheh inanloo hajiloo parseh pathobiology & genetics laboratory, tehran, iran.

small supernumerary marker chromosomes (ssmc) are still a major problem in clinical cytogenetics as they cannot be identified or characterized unambiguously by conventional cytogenetics alone. on the other hand, and perhaps more importantly in prenatal settings, there is a challenging situation for counseling how to predict the risk for an abnormal phenotype, especially in cases with a de novo ...

Journal: :Journal of pediatric genetics 2015
Marine Manvelyan Izabella Simonyan Galina Hovhannisyan Rouben Aroutiounian Ahmed B Hamid Thomas Liehr

Complex small supernumerary marker chromosomes (sSMCs) constitute one of the smallest subsets within the patients with an sSMC. Complex sSMCs consist of chromosomal material derived from more than one chromosome, for example, the derivative der(22)t(11;22)(q23;q11.2) in Emanuel syndrome. Here, a yet unreported case of a complex sSMC formed due to a t(7;9)(p22;q22)mat is presented.

2016
Dina F. Ahram Danae Stambouli Aleksandra Syrogianni Yasser Al‐Sarraj Spyridon Gerou Hatem El‐Shanti Marios Kambouris

Various chromosomal anomalies including small supernumerary marker chromosome (sSMC) and Uniparental disomy (UPD) have been described in association with intellectual disability and autism spectrum disorder. Based on our reported findings, we recommend that patients with sSMC(8) be evaluated for autism spectrum disorder (ASD) for early institution of therapy. In the presence of an identifiable ...

Journal: :Cytogenetic and genome research 2007
T Liehr G E Utine U Trautmann A Rauch A Kuechler J Pietrzak E Bocian N Kosyakova K Mrasek K Boduroglu A Weise D Aktas

Here we report on three new patients with neocentric small supernumerary marker chromosomes (sSMC) derived from chromosome 2, 13 and 15, respectively. The sSMC(13) and sSMC(15) had inverted duplicated shapes and the sSMC(2) a ring chromosome shape. All three cases were clinically severely abnormal. A review of the available sSMC literature revealed that up to the present 73 neocentric sSMC case...

Journal: :The West Indian medical journal 2012
T Gulten O Gorukmez M Karkucak M Ture T Yakut

Marker chromosomes are very rare in Klinefelter patients and phenotypic findings are related to the affected chromosomal region. The phenotypic effects of small supernumerary marker chromosomes (sSMC) range from multiple malformations/mental retardation to no effect (ie a normal phenotype). This wide spectrum of phenotypes is due to the origin, structure and gene content of the marker chromosom...

Small supernumerary marker chromosomes (sSMCs), or markers, are abnormal chromosomal fragments that can be hereditary or de novo. Despite the importance of sSMCs diagnosis, de novo sSMCs are rarely detected during the prenatal diagnosis process. Usually, prenatally diagnosed de novo sSMCs cannot be correlated with a particular phenotype without knowing their chromosomal origin and content; ther...

Journal: :International journal of molecular medicine 2008
Marina Manvelyan Mariluce Riegel Monica Santos Carme Fuster Franck Pellestor Marie-Luise Mazaurik Bernt Schulze Anna Polityko Hanne Tittelbach Gisela Reising-Ackermann Britta Belitz Ute Hehr Christina Kelbova Marianne Volleth Elisabeth Gödde Jasen Anderson Peter Küpferling Sigrid Köhler Hans-Christoph Duba Andreas Dufke Dilek Aktas Thomas Martin Isolde Schreyer Elisabeth Ewers Daniela Reich Kristin Mrasek Anja Weise Thomas Liehr

Thirty-two patients with fertility problems were identified as carriers of small supernumerary marker chromosomes (sSMC). Molecular cytogenetic techniques were used to characterize their chromosomal origin. Together with the other cases available in the literature 111 sSMC cases have now been detected in connection with fertility problems in otherwise clinically healthy persons and characterize...

Journal: :Prenatal diagnosis 2006
Chyi-Chyang Lin Yao-Yuan Hsieh Chung-Hsing Wang Yueh-Chun Li Lie-Jiau Hsieh Chien-Chung Lee Chang-Hai Tsai Fuu-Jen Tsai

OBJECTIVE To present prenatal findings and molecular cytogenetic characterization of a small supernumerary marker chromosome (sSMC) derived from chromosome 22 with apparently normal phenotype. CASE AND METHODS An amniocentesis was performed at 15 weeks' gestation and a small marker chromosome in the female fetus of a twin pregnancy was noted. A second amniocentesis was performed at 18 weeks; ...

2015
Marta Olszewska Elzbieta Wanowska Archana Kishore Nataliya Huleyuk Andrew P. Georgiadis Alexander N. Yatsenko Mariya Mikula Danuta Zastavna Ewa Wiland Maciej Kurpisz

Chromosomes occupy specific distinct areas in the nucleus of the sperm cell that may be altered in males with disrupted spermatogenesis. Here, we present alterations in the positioning of the human chromosomes 15, 18, X and Y between spermatozoa with the small supernumerary marker chromosome (sSMC; sSMC(+)) and spermatozoa with normal chromosome complement (sSMC(-)), for the first time describe...

Journal: :Cytogenetic and genome research 2011
T Liehr I Bartels B Zoll E Ewers K Mrasek N Kosyakova M Merkas A B Hamid F von Eggeling N Posorski A Weise

Unbalanced chromosomal abnormalities (UBCA) are reported for >50 euchromatic regions of almost all human autosomes. UBCA are comprised of a few megabases of DNA, and carriers are in many cases clinically healthy. Here we report on a partial trisomy of chromosome 4 of the centromere-near region of the short arm of chromosome 4 present as a small supernumerary marker chromosome (sSMC). The sSMC w...

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