نتایج جستجو برای: shprintzen syndrome

تعداد نتایج: 621913  

2016
Sankalp Yadav Gautam Rawal

Shprintzen-Goldberg Syndrome is an extremely infrequent disorder of connective tissue, characterized by craniosynostosis and marfanoid features, also known as Marfanoid Craniosynostosis syndrome. The syndrome was first introduced by Sugarman and Vogel' (1981) however, Shprintzen and Goldberg established this as a separate clinical entity in the year 1982. Since then, approximately sixty such ca...

Journal: :iranian journal of child neurology 0
shadab salehpour 1. department of pediatrics, mofid children hospital, faculty of medicine, shahid beheshti university of medical sciences, tehran, iran feyzollah hashemi-gorji 2. genomic research center, shahid beheshti university of medical sciences, tehran, iran ziba soltani 2. genomic research center, shahid beheshti university of medical sciences, tehran, iran soudeh ghafouri-fard 3. department of medical genetics, shahid beheshti university of medical sciences, tehran, iran mohammad miryounesi 2. genomic research center, shahid beheshti university of medical sciences, tehran, iran

abstract goldberg-shprintzen syndrome (omim 609460) (goshs) is an autosomal recessive multiple congenital anomaly syndrome distinguished by intellectual disability, microcephaly, and dysmorphic facial characteristics. most affected individuals also have hirschsprung disease and/or gyral abnormalities of the brain. this syndrome has been shown to be associated with kiaa1279 gene mutations at 10q...

Journal: :Meandros Medical and Dental Journal 2018

Journal: :Case Reports in Orthopedics 2020

Journal: :Journal of the College of Physicians and Surgeons Pakistan 2019

Journal: :The Australasian medical journal 2014
Bhushan Shah Suman Sahu Piyush Kalakoti Sankalp Yadav M M Aarif Syed Venugopal Brijmohan Bhattad Meena Shaikh

Shprintzen-Goldberg syndrome (S-G) is a rare connective tissue disorder characterised by craniosynostosis, craniofacial dysmorphism, skeletal, cardiovascular, neurological, and other abnormalities. We herein present a case of a five-year-old Indian child who presented to our clinic with reducible umbilical hernia since birth, mental retardation, and delayed developmental milestones. After metic...

Journal: :Journal of medical genetics 1993
J Burn A Takao D Wilson I Cross K Momma R Wadey P Scambler J Goodship

The conotruncal anomaly face syndrome was described in a Japanese publication in 1976 and comprises dysmorphic facial appearance and outflow tract defects of the heart. The authors subsequently noted similarities to Shprintzen syndrome and DiGeorge syndrome. Chromosome analysis in five cases did not show a deletion at high resolution, but fluorescent in situ hybridisation using probe DO832 show...

Journal: :Journal of Evolution of Medical and Dental Sciences 2016

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