Pleuropulmonary blastoma is one of the rarest tumours occurring in childhood. The pathogenesis and therapeutic management of this condition remain controversial. We report the case of an 8-month-old girl with cystic pleuropulmonary blastoma (type 1), presenting with respiratory distress and a tension pneumothorax. The clinical and radiological aspects of the pleuropulmonary blastoma are also di...

INTRODUCTION Pleuropulmonary blastoma is a very rare, aggressive, embryonal pulmonary neoplasm which mostly affects children under the age of 5. According to the histopathological features, three subtypes of pleuropulmonary blastoma have been recognized: type I (purely cystic), type II (grossly visible cystic and solid elements) and type III (purely solid). Characteristics of type I and type II...

BACKGROUND In children, acute affectation of the thorax is presented during pleuropulmonary infection, bronchopulmonary malformation and malignant tumors. We had the opportunity to treat patients with malignant tumors in the thorax and we present our findings. CLINICAL CASES We studied three patients with the diagnosis of pleuropulmonary blastoma. All patients were being treated with surgical...

Pleuropulmonary blastoma is a rare childhood neoplasm accounting for less than one percent of all primary malignant lung tumors of children less than six years of age. Metastasis to CNS, orbit and iris, bone, contralateral lung and rarely adrenal glands, liver, kidney and pancreas has been described. This report presents a rare case of pleuropulmonary blastoma with cervical lymph node metastasi...

The case of 38-month-old boy is being reported who was brought to the pediatrics clinic with fever, cough, hemoptysis, and breathing difficulty. Imaging studies revealed a right lower chest mass. Lobectomy and histopathological examination revealed it to be predominantly solid pleuropulmonary blastoma type II. It is a rare pediatric pleuropulmonary tumor with aggressive behavior and tendency to...

Pulmonary blastoma (PB) is a rare form of lung tumour and is accountable for 0.25-0.5% of primary pulmonary malignancies. Initially pulmonary blastoma was divided into three subtypes: biphasic pulmonary blastoma (BPB) consisting of an epithelial and mesenchymal component, well differentiated fetal adenocarcinoma (WDFA) built of well differentiated epithelium and a mesenchymal component and mali...