A lymphangioma is a benign proliferation of lymph vessels, producing fluid-filled cysts that result from a blockage of the lymphatic system. The incidence of abdominal lymphangiomas is unknown; however they account for from 3% to 9.2% of all pediatric lymphangiomas, with retroperitoneal lymphangioma representing less than 1% of abdominal lymphangiomas. Due to rarity, preoperative diagnosis is o...

Address correspondence to: Dr. Ajay Rana, Connecticut Children’s Medical Center, 282 Washington Street, Hartford, CT 06106; Tel: 860-545-9563; Fax: 860-545-9561; E-mail: [email protected]. Cystic lymphangiomas are rare in children. They commonly present as neck or axillary masses and only rarely involve the gastrointestinal tract. The clinical presentation of these tumors depends on their size...

Hepatic lymphangiomas are extremely rare; moreover cystic lymphangiomas usually arise in areas such as the neck and axilla, where loose connective tissue allows the expansion of lymphatic channels. The case of a 65-year old male is described, who presented with a solitary lymphangioma in the liver. The lesion was discovered incidentally and due to diagnostic uncertainty was removed surgically. ...

Combined/complex malformations Klippel-Trenaunay syndrome (capillary-lymphatico-venous malformation) Proteus syndrome Maffucci syndrome Table 110.1: Classification of lymphatic malformations. Introduction Lymphangiomas are developmental defects of the lymphatic channels that belong to a large spectrum of vascular malformations. They are most commonly located in the head and neck region, and to ...

Intraabdominal lymphangiomas are rare. A five-year-old girl with abdominal lymphangiomas was successful treated by excision of the mass and resection of short segment of small bowel. We present a case report.

Lymphangiomas are hamartomatous lymphatic mutations that happen when tissue is sequestered at few areas not associated with channels. Lymphatic malformations of the head and neck, additionally called lymphangiomas or cystic hygromas, a diverse group lesions. The majority present birth, 90% developing before age two. As much as 75% these arise within neck region less frequently stated oral cavit...

A case report of bilateral lymphangiomas of the mandibular alveolar ridge in the neonate is presented. This case is of interest in that it constitutes the first report of multiple lymphangiomas occurring within a single dental quadrant. Lymphangiomas generally are regarded as hamartomas and as such represent a developmental malformation of lymphatic vessels. The most common intraoral site of ly...

OBJECTIVE: To describe the results of the use of alpha-2a-interferon in the treatment of inoperable childhood lymphangiomas refractory to other therapeutic management. METHOD: We reviewed the literature about pathogenic events and the treatments available for lymphangiomas. Based on that, we used alpha-2a-interferon at a dose of 3 million units/m(2)/day administered subcutaneously to patients w...

Introduction Lymphangiomas are rare benign tumors. They are preferentially located in the head, neck, and axilla in children.[1] However, lymphangiomas in the peritoneal cavity are extremely rare, particularly in adults. In the abdomen, lymphangiomas occur most commonly in the mesentery, followed by the omentum, mesocolon, and retroperitoneum. The etiology is unclear, but they are considered pr...