Figure 1. Radiograph of N.D. preoperatively, demonstrating thumb hypoplasia and an unstable carpometacarpal joint. Figure 2. Schematic of the hand with hypoplastic thumb to be amputated (dashed lines).

This chapter emphasizes the dilemma of salvage and reconstruction of the congenitally aplastic or hypoplastic thumb without normal cerebrocortical representation for prehensile grasp and pinch. The philosophy of reconstruction of the congenitally anomalous thumb is clearly divergent from thumb reconstruction following trauma. It is difficult to advise parents who seek surgical correction of the...

the yunis-varón syndrome represents a rare autosomal recessive syndrome of easy recognition characterized by defective growth of the cranial bone along with complete or partial absence of the clavicles (cleidocranial dysplasia), absence of thumbs and halluces, distal aphalangia, ectodermal anomalies, growth retardation and poor outcome. the molecular genetic basis is unknown. here, we report an...

this deformity is often reffered to as thumbclutched hand, but a better term is the congenital clasped thumb. the congenital clasped thumb is associated with several well-de-fined syndromes, although it may also present as an isolated abnormality. weckesser, reac, and heiple called it a syndrome and divided the syndrome in to four groups. in group i, the thumb is deficient in extention only. in...

While rarely seen in the present-day Western world, phocomelia is not uncommon in underdeveloped countries. Phocomelia is an abnormality in which the limbs are not fully formed. It may be inherited as an autosomal recessive or dominant disorder. This case concerns a 12-year-old Afghan boy with multiple skeletal anomalies, most prominently of his right arm, including aplasia of the entire proxim...

The use of the abductor digiti minimi transfer to restore opposition in patients with hypoplasia of the thumb has been widely described in the literature. It has been found to be effective in restoring abduction, but less so in restoring the rotational component of opposition. In cases where there is concomitant supination of the thumb, abductor digiti minimi transfer alone would not result in ...

The aim of pollicisation is to provide a strong, stable and mobile thumb of optimal size and shape. The controlling factors are the quality of the index finger, the quality of the adjacent digits and the stability and mobility of the wrist, all of which will be compromised by hypoplasia of bones, joints and soft tissues. However, even a stiff, bent, hypoplastic index finger accompanying a forea...