introduction tetralogy of fallot (tof) in the absent of pulmonary valve is a rare congenital anomaly (3%of tof patients). case presentation we are presenting an 18- year-old male with history of dyspnea on exertion and cyanosis since childhood. despite the diagnosis of congenital heart disease, no intervention was done due to his poor socioeconomic culture. at age of 18, he referred to our cent...

Two cases are described of a most unusual variant of two-chambered right ventricle. In both the ventricular septal defect was between the distal chamber of the right ventricle and the left ventricle. However the extensive dividing 'septum' between proximal and distal parts of the right ventricle converted the latter, haemodynamically, into part of the left ventricle. In the first case the dista...

the majority of coronary artery fistulas (cafs) are congenital. the anomaly accounts for 0.4% of congenital heart defects and approximately 50% of pediatric coronary vasculature anomalies. twenty percent of people with congenital cafs have other concomitant cardiac anomalies, most frequently aortic and pulmonary atresia and patent ductus arteriosus. it is worthy of note that caf with the tetral...

To examine the excitation of the double chamber right ventricle and the possibility that it results from a displaced, hypertrophied moderator band, seven patients with double chamber right ventricle were studied. All seven had pre- and postoperative electrocardiograms. Intraoperative right ventricular epicardial maps were obtained in three; right ventricular endocardial activation maps performe...

This paper describes two pathological specimens of congenital heart disease with double inlet right ventricle in which the ventricular chamber receives the right atrioventricular ostium and partially the left atrioventricular ostium, the two atrioventricular ostia being completely separated. The published reports are reviewed and only cases of double inlet left ventricle have been found. An ont...

Rev Esp Cardiol. 2005;58(2):217 217 We report the case of a 56-year-old asymptomatic man with a pulmonary grade III/VI holosystolic murmur. No electrocardiographic changes were observed. On echocardiography, the left ventricle was normal with normal systolic function, and the right ventricle (RV) was hypertrophic with a midventricular gradient (maximum, 56; mean, 33 mm Hg) and a perimembranous ...