نتایج جستجو برای: dfna

تعداد نتایج: 14  

2011
Suphat Korkiatithaweechai Pornpusadee Umsarika Narong Praphairaksit Nongnuj Muangsin

The controlled release of diclofenac sodium (DFNa) from a chitosan-oxidized konjac glucomannan (CTS-OKG) polymer film was studied. Konjac glucomannan (KGM) was initially oxidized by sodium periodate and then cross-linked to CTS via imine bonds (-C=N-) to form the new CTS-OKG copolymer. The DFNa loaded CTS-OKG polymers were characterized by Fourier transformed infrared spectroscopy (FT-IR) and X...

2014
Yu Su Wen-Xue Tang Xue Gao Fei Yu Zhi-Yao Dai Jian-Dong Zhao Yu Lu Fei Ji Sha-Sha Huang Yong-Yi Yuan Ming-Yu Han Yue-Shuai Song Yu-Hua Zhu Dong-Yang Kang Dong-Yi HAN Pu Dai

TECTA-related deafness can be inherited as autosomal-dominant nonsyndromic deafness (designated DFNA) or as the autosomal-recessive version. The α-tectorin protein, which is encoded by the TECTA gene, is one of the major components of the tectorial membrane in the inner ear. Using targeted DNA capture and massively parallel sequencing (MPS), we screened 42 genes known to be responsible for huma...

پایان نامه :وزارت علوم، تحقیقات و فناوری - دانشگاه علوم بهزیستی و توانبخشی 1389

ناشنوایی یک اختلال رایج حسی – عصبی در تمامی سنین می باشد که توسط عوامل محیطی ، ژنتیکی یا هر دو ایجاد می شود.از آنجا که این اختلال بسیار هتروژن بوده ،اساس ژنتیکی آن بسیار پیچیده است.تقریبا 70 درصد موارد ناشنوایی ارثی ، غیر سندرومی می باشد. این دسته از ناشنوایی بر اساس الگوی وراثتی ، به چهار نوع تقسیم می گردد: اتوزومی مغلوب(75-85%) ، اتوزومی غالب (15-25% )، وابسته به جنس و میتو- کندریایی( <1%). ...

Journal: :Journal of medical genetics 2003
E Flex M Mangino M Mazzoli A Martini V Migliosi A Colosimo R Mingarelli A Pizzuti B Dallapiccola

Hearing impairment (HI) is the most frequent sensory defect with wide genetic heterogeneity. Approximately 80% of genetic hearing loss is non-syndromic and 15-25% of exhibit autosomal dominant inheritance. We analysed an Italian three generation family in which non-syndromic hearing impairment is transmitted as an autosomal dominant trait. Onset of HI in all affected subjects occurred in the se...

Journal: :Journal of medical genetics 2004
S Modamio-Høybjør M A Moreno-Pelayo A Mencía I del Castillo S Chardenoux D Morais M Lathrop C Petit F Moreno

P rogressive hearing loss is a significant problem in all ageing populations. By the age of 80 years, nearly 50% of individuals have hearing loss that impairs their ability to communicate easily, leading to increasing social isolation. Progressive hearing loss in middle and late adulthood is considered multifactorial, with involvement of both genetic and environmental factors. In contrast, chil...

2003
M A Moreno-Pelayo

A pproximately 1 in 1000 children is born with a serious permanent hearing impairment (pre-lingual deafness), and it is estimated that more than half of these cases in developed countries are due to genetic factors. The prevalence of hearing loss increases dramatically with age; it is estimated that approximately 5% of people under 45 years of age have a significant loss of hearing, increasing ...

2015
Mette Nyegaard Nanna D. Rendtorff Morten S. Nielsen Thomas J. Corydon Ditte Demontis Anna Starnawska Anne Hedemand Annalisa Buniello Francesco Niola Michael T. Overgaard Suzanne M. Leal Wasim Ahmad Friedrik P. Wikman Kirsten B. Petersen Dorthe G. Crüger Jaap Oostrik Hannie Kremer Niels Tommerup Morten Frödin Karen P. Steel Lisbeth Tranebjærg Anders D. Børglum Marci Lesperance

Nonsyndromic hearing impairment (NSHI) is a highly heterogeneous condition with more than eighty known causative genes. However, in the clinical setting, a large number of NSHI families have unexplained etiology, suggesting that there are many more genes to be identified. In this study we used SNP-based linkage analysis and follow up microsatellite markers to identify a novel locus (DFNA66) on ...

2013
Yali Zhao Feifan Zhao Liang Zong Peng Zhang Liping Guan Jianguo Zhang Dayong Wang Jing Wang Wei Chai Lan Lan Qian Li Bing Han Ling Yang Xin Jin Weiyan Yang Xiaoxiang Hu Xiaoning Wang Ning Li Yingrui Li Christine Petit Jun Wang Huanming Yang Jian Wang Qiuju Wang

In this study, a five-generation Chinese family (family F013) with progressive autosomal dominant hearing loss was mapped to a critical region spanning 28.54 Mb on chromosome 9q31.3-q34.3 by linkage analysis, which was a novel DFNA locus, assigned as DFNA56. In this interval, there were 398 annotated genes. Then, whole exome sequencing was applied in three patients and one normal individual fro...

Journal: :Journal of medical genetics 2003
M A Moreno-Pelayo S Modamio-Høybjør A Mencía I del Castillo S Chardenoux M Fernández-Burriel M Lathrop C Petit F Moreno

A pproximately 1 in 1000 children is born with a serious permanent hearing impairment (pre-lingual deafness), and it is estimated that more than half of these cases in developed countries are due to genetic factors. The prevalence of hearing loss increases dramatically with age; it is estimated that approximately 5% of people under 45 years of age have a significant loss of hearing, increasing ...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید