Congenital diaphragmatic hernia (CDH) is a rare condition. The reported incidence of intrathoracic renal ectopia due to CDH is also rare. A right-sided thoracic kidney is much less common due to the location of the liver. Isolated intrathoracic kidney is usually asymptomatic and diagnosed incidentally on chest imaging. The authors report on a 21days old female infant with late-presenting right ...

Congenital diaphragmatic hernia / hiatal (Congenital Diaphragmatic Hernia CDH) alters normal cardiopulmonary physiology in neonates or pediatric patients due to pressure from the abdomen into thoracic cavity. The open surgical and laparoscopic approaches pose challenges for anesthesiologist team because of complications CDH surgery itself. We present a case successful anesthetic management 2-ye...

Congenital diaphragmatic hernia (CDH) is a rare congenital anomaly of the diaphragm with an incidence of 1:2000-5000 of live births. This study retrospectively evaluated patients who had been operated on for CDH at our department of Pediatric Surgery between January 2013 and December 2016. The Demographic Data and outcomes of right CDH cases (Group 1) were compared with left CDH cases (Group 2).

Incidence Congenital diaphragmatic hernia (CDH) refers to a congenital defect in the posterolateral diaphragm at the “foramen of Bochdalek.” It is a relatively common cause of neonatal respiratory distress with an overall incidence between 1:2000 and 1:5000 live births. CDH accounts for about 90% of congenital diaphragmatic defects. Eighty to ninety percent of congenital diaphragmatic hernias o...

Fryns syndrome is characterized by multiple congenital anomalies including congenital diaphragmatic hernia (CDH), and congenital heart disease (CHD).The prognosis of infant with Fryns syndrome and left sided CDH when associated with pulmonary hypoplasia is grave. We report a 2year old boy with Fryns syndrome who had right sided CDH, Tetralogy of Fallot, and other multiple congenital anomalies. ...

Congenital diaphragmatic hernia (CDH) is a congenital disorder characterized by defect in the diaphragm, which causes contents of stomach to protrude into chest cavity. Increased survival CDH patients related initial management form ventilator strategy, pulmonary hypertension, improvement surgical and anesthetic techniques, use extracorporeal membrane oxygenation (ECMO) when indicated. Early st...

Fryns syndrome is an autosomal recessive hereditary disease, including abnormal facies, small thorax with widely spaced hypoplastic nipples, distal limb and nail hypoplasia, and diaphragmatic hernia with pulmonary hypoplasia. The aim of the present report is to increase awareness of Fryns syndrome and its association with rare abnormalities such as cecal duplication cyst, horseshoe kidney and b...

Bilateral congenital diaphragmatic hernia (CDH) is a rare birth defect, with a poor prognosis. We describe a case of bilateral CDH discovered while repairing the right sided CDH. Diaphragmatic defect was repaired and a silo was applied on the abdominal wound to avoid abdominal compartment syndrome. The patient however died postoperatively due to severe pulmonary hypertension.

Congenital diaphragmatic hernia (CDH) is often diagnosed and treated in the perinatal period. Recurrence a known complication that may very rarely occur years after operation. We report here case of patient who had an operation for CDH at birth then recurred adulthood. Given risk complications symptomatology patient, we decided to treat surgically. successfully performed video-assisted thoracic...

Congenital diaphragmatic hernia (CDH) is a developmental defect that accounts for 8% of all major congenital anomalies and is associated with a high mortality rate despite optimal postnatal treatment. Its etiology is uncertain. We report a case of familial CDH in a Taiwanese family. We believe autosomal recessive inheritance is the possible genetic etiology of CDH in this family.