glanzmann's thrombasthenia (gt) is a rare, genetically inherited platelet disorder in which the platelet glycoprotein iib/iiia (gp iib/iiia) complex is either deficient or, dysfunctional. the incidence is about 1 in 1,000,000. this case report deals with a 4 year-old girl diagnosed with gt presenting with dental caries and periapical lesions in the primary mandibular first molars. to provide th...

ectodermal dysplasia is a hereditary disorder associated with abnormal development of embryonic ectodermally-derived organs including teeth, nails, hair and sweat glands. hypodontia of the primary and permanent dentition is the most common oral finding. therefore, affected patients need dental prosthetic treatments during their developmental years. this report presents two cases of children aff...

Ectodermal Dysplasia is a hereditary disorder commonly associated with trichodysplasia (abnormal hair), onchodysplasia nails), dyshidrosis or missing sweat glands) and abnormal dentition. Due to ectodermal dysplasia, for missing, abnormally shaped, mal-positioned teeth, wide range of prosthetic options are available oral rehabilitation. This case report represents prosthodontic rehabilitation c...

The authors have presented a technique of full occlusal rehabilitation in a case of severe dental fluorosis. In this technique, maxillary and mandibular anterior teeth were simultaneously prepared and restored first. This was followed by simultaneous preparation of maxillary and mandibular posterior teeth that were restored in canine guided occlusion. The technique and sequence followed here is...

BACKGROUND Advances made in prevention have helped postpone complete edentulism in older patients. However, in the elderly, the physiological state reduces patients' ability to adapt to oral rehabilitation and degrades the patient's oral condition. Consequently, elderly edentulous subjects avoid many types of foods, which can lead to substantial nutritional consequences. Complete dentures retai...

an abnormally small oral orifice is defined as microstomia. microstomia may result from epidermolysis bullosa (eb), which consists of a group of disorders characterized by the presence of mechanical fragility of the skin with recurrent development of blisters and vesicles, resulting from minor mechanical friction or trauma. since such patients have a small oral aperture, it may be impossible to...

Ectodermal dysplasia is a hereditary disorder that occurs as a consequence of disturbances in the ectoderm of the developing embryo. The triad of nail dystrophy, alopecia or hypotrichosis and palmoplantar hyperkeratosis is usually accompanied by a lack of sweat glands and a partial or complete absence of primary and/or permanent dentition. Two case reports illustrating the prosthetic rehabilita...