how to cite this article: abdi m, khatami sh, hakhamaneshi ms, alaei mr, azadi na, zamanfar d, taghikhani m.validation of urinary glycosaminiglycans in iranian patients with mucopolysaccharidose type i: the effect of urine sedimentation characteristics. iran j child neurol. 2014; 8(4):39-45.   abstract objective the first line-screening test for mucopolysaccharidosis is based on measurement of ...

The early and accurate diagnosis of the mucopolysaccharidoses remains a problem for the clinical laboratory. Reported here is the systematic compari­ son of the ability of three common glycosaminoglycanuria screening proce­ dure (the Berry spot test, the AMES MPS® spot test, and the gross acid albumin turbidity test) to detect the mucopolysaccharidoses. These tests were run on random urine samp...

how to cite this article: ashrafi mr, tavasoli ar. infantile-onset pompe disease. iran j child neurol autumn 2012; 6:4(suppl. 1):7-9. pls see pdf.   refe r ences: 1. kishnani ps, steiner rd. pompe disease diagnosis and management guidelines. american j med genetic. 2006 .vol; 8; no5. 2. case se, beckemyer aa. infantile pompe disease on ert-updateonclinicalpresentation,musculoskeletal management...

The article has indicated the principle scheme for post-harvest processing of cultural berries according to the possibilities of the developed new berry sorter. The article tackles the constructive features of the post-harvest treatment of berries as well as of the belt sorter that functions on the principle of successive sorting method. The aim of study was to evaluate the technological featur...

to evaluate effects of gibberllic acid, gridling, berry and bunch thining and their combination on fruit maturity, berry and bunch characteristics of grape cv. yaqooti an experiment was carried out using randomized complete block design with three replications in kavar, shiraz, iran, in 2010-2011 growing season. each experimental plot consisted of three vines. treatments included: t1: gibberlli...

OBJECTIVE The first line-screening test for mucopolysaccharidosis is based on measurement of urinary glycosaminoglycans. The most reliable test for measurement of urine glycosaminoglycans is the 1,9-dimethyleneblue colorimetric assay. Biological markers are affected by ethnical factors, for this reason, the World Health Organization recommends that the diagnostic test characteristics should be ...