developmental venous anomaly (dva) is a common lesion formerly known as venous angioma. dvas drain normal brain parenchyma; however, parenchymal abnormalities surrounding dvas have been reported. unilateral putamen and caudate calcification in the drainage territory of dvas has so far been reported in 7 cases, all with deep venous drainage. we present two additional cases of dvas, one with supe...

the clinical and phenotypic features of two siblings (a 12 years old girl and her 7 year old brother) with cockayne syndrome are described. the main problems were mild to moderate mental retardation, dwarfism, clumsy gait, photosensitive skin lesions and progeroid (senile like) appearance. brain ct - scans revealed symmetrical, well defined areas of calcification mainly located at lenticular nu...

Fahr syndrome is a rare anatomo-clinical entity in pediatrics. Associating calcifications of the basal ganglia with phospho-calcium metabolism disorders, most often resulting neuropsychiatric symptoms. In our study, discovery this two patients was fortuitous thanks to typical radiological appearance, associated clinical picture they initially presented, hence interest brain imaging diagnosis sy...

Fahr's phenomenon is a rare neurological disorder characterized by calcifications of several structurers the human brain, including basal ganglia, dentate nuclei cerebellum, thalamus, and hippocampus. It may exist in an idiopathic form or it can be associated to calcium dysmetabolism due parathormone (PTH) defect signaling. Symptoms span from parkinsonism psychiatric syndromes, ataxia, convulsi...

INTRODUCTION Fahr's disease is characterized by bilateral calcium deposition within the basal ganglia, cerebellar dentate nucleus and subcortical brain white matter. The main clinical manifestations are rigid or hyperkinetic syndrome, mood disorders and cognitive impairment. The correlation between neurological impairment and symmetrical basal ganglia calcification is not so frequent. Aim of th...

Fahrs syndrome is a rare anatomoclinical entity whose main etiology primary or postoperative hypoparathyroidism. It characterized by bilateral and symmetrical intracerebral calcifications, localized in the basal ganglia. Hypoparathyroidism, postoperative, most classic anomaly. Hyperparathyroidism exceptionally reported as cause of Fahr syndrome. We report case 30-year-old woman who presented wi...

PURPOSE To review the cranial CT and MR examinations of 29 children with perinatally transmitted HIV infection and correlate the imaging findings with clinical and pathologic data. METHODS 28 children were examined with CT, four with MR. RESULTS CT abnormalities were seen in 25 children studied (89%), including cerebral atrophy (25 children), basal ganglia calcification (10 children), periv...

BACKGROUND Fahr's disease is rare a neurodegenerative idiopathic condition characterized by symmetric and bilateral calcifications of basal ganglia, usually associated with progressive neuropsychiatric dysfunctions and movement disorders. The term "Fahr's syndrome" is used in presence of calcifications secondary to a specific cause, but the variability of etiology, pathogenesis, and clinical pi...

Developmental venous anomaly (DVA) is a common lesion formerly known as venous angioma. DVAs drain normal brain parenchyma; however, parenchymal abnormalities surrounding DVAs have been reported. Unilateral putamen and caudate calcification in the drainage territory of DVAs has so far been reported in 7 cases, all with deep venous drainage. We present two additional cases of DVAs, one with supe...