Fahr's disease is a rare syndrome characterized by symmetrical and bilateral intracranial calcifications. We report a 21-year-old male who presented with aggression, talkativeness, restlessness, and insomnia of recent onset. His neurological examination was normal. Mental status examination and clinical investigation revealed mania. Brain revealed symmetrical large areas and foci of calcificati...

A 43-year-old man who had been treated for a craniopharyngioma with surgery and radiotherapy (33 years ago) was referred for evaluation of a sudden hemiparesis. Neuroimaging documented a brainstem cavernoma associated with basal ganglia calcifications and white matter hyperintensity near anterior temporal lobe cysts (Figures 1 and 2). Late brain abnormalities are often observed after radiothera...

Fahr's disease or Fahr's syndrome is a rare neurodegenerative disorder characterized by abnormal symmetrical calcifications of the basal ganglia, thalami, sub-cortical hemispheric white matter and deep cerebellar nuclei. It can be idiopathic or associated with an endocrinopathy, frequently with parathyroid disorder. Clinical spectrum of the disease is wide ranging from neurological features lik...

 ABSTRACT Background: High resolution CT scan has made early diagnosis of intraventricular hemorrhage (IVH) easier. Posttraumatic intraventricular hemorrhage has been reported to a greater extent because of the CT scan. Methods: 904 patients were admitted in the NSICU from March 2001 to March 2002 with severe closed head injury, of those only 31 patients with intraventricular hemorrhage (GCS le...

Neurological tumors, such as gliomas and meningiomas are rarely presented by movement disorders. Early detection of neurological both basal ganglia arising tumors ganglia-sparing ones, presenting with disorders is crucial to prevent any further deficits.

RATIONALE Pediatric idiopathic hypoparathyroidism with extensive intracranial calcifications outside the basal ganglia (BG) is extremely rare with less than 10 cases worldwide. PATIENT CONCERNS An 11-year-old Saudi male child presented with tetany with otherwise normal neurological and other body system examination diagnoses severe hypocalcemia for differential diagnosis. INTERVENTIONS Furt...

There is a growing interest in defining the genetic background of autosomally dominant inherited Familial Idiopathic Basal Ganglia Calcification (FIBGC), a neuropsychiatric condition often described as ‘‘Fahr’s Disease’’ [1–3]. However, the current debate about the nosology of this heterogeneous phenotype demands a search for standard diagnostic criteria and the identification of loci or mutati...

Objectives: To mathematically model the oscillatory behaviour of Basal Ganglia for Parkinson’s disease as well to simulate by using Cell designer and Scilab. Method: The pathway Parkinsons was downloaded from KEGG database studied scilab programming cell tool. In this work, loaded designer, that is working on basis systems biology mark-up language, analysed entire pathway. Findings: oscillary b...

normal 0 false false false en-us x-none fa background : fahr's disease is a rare neurodegenerative disorder of unknown cause characterized by idiopathic basal ganglia calcification that is associated with neuropsychiatric and cognitive impairment. no case of fahr's disease with associated cardiac conduction disease has been described in the literature to date. the objective of this case report ...