نتایج جستجو برای: idiopathic hypogonadotropic hypogonadism

تعداد نتایج: 66457  

Journal: :Human reproduction 2006
Pananghat A Kumar Nelly Pitteloud Peter A M Andrews Andrew Dwyer Frances Hayes William F Crowley Martin Dym

BACKGROUND Adult patients with idiopathic hypogonadotropic hypogonadism (IHH) typically present with absent puberty and therefore have prepubertal testes. IHH is recognized as one of the few curable causes of male infertility and is often effectively treated with either gonadotropins or pulsatile GnRH therapy. The objective of this study was to determine the structure of the testis prior to ini...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2007
J Larry Jameson

W orldwide, puberty is recognized by various cultures and celebrated as a rite of passage into adulthood. The methodical drumbeat of these religious and social ceremonies foreshadows the rhythm of reproduction that, in many ways, marks the final stage of development. Despite its social and physiological significance, including perpetuation of the species, the pathways that regulate the onset of...

Journal: :Arquivos brasileiros de endocrinologia e metabologia 2012
Cintia Tusset Sekoni D Noel Ericka B Trarbach Letícia F G Silveira Alexander A L Jorge Vinicius N Brito Priscila Cukier Stephanie B Seminara Berenice B de Mendonça Ursula B Kaiser Ana Claudia Latronico

OBJECTIVE To investigate the presence of variants in the TAC3 and TACR3 genes, which encode NKB and its receptor (NK3R), respectively, in a large cohort of patients with idiopathic central pubertal disorders. SUBJECTS AND METHODS Two hundred and thirty seven patients were studied: 114 with central precocious puberty (CPP), 73 with normosmic isolated hypogonadotropic hypogonadism (IHH), and 50...

2016
Mehmet Nuri Özbek Hüseyin Demirbilek Rıza Taner Baran Ahmet Baran

OBJECTIVE Deficiency of sex steroids has a negative impact on bone mineral content. In studies conducted on postmenopausal women and animal studies, elevated follicle-stimulating hormone (FSH) levels were found to be correlated with a decrease in bone mineralization and osteoporosis. The aim of the present study was to evaluate bone mineral density (BMD) in adolescent girls with hypogonadotropi...

Journal: :Translational Andrology and Urology 2021

2017
A. Kemal Topaloğlu

Traditionally, idiopathic hypogonadotropic hypogonadism (IHH) is divided into two major categories: Kallmann syndrome (KS) and normosmic IHH (nIHH). To date, inactivating variants in more than 50 genes have been reported to cause IHH. These mutations are estimated to account for up to 50% of all apparently hereditary cases. Identification of further causative gene mutations is expected to be mo...

Journal: :The Journal of clinical investigation 2007
Nelly Pitteloud Richard Quinton Simon Pearce Taneli Raivio James Acierno Andrew Dwyer Lacey Plummer Virginia Hughes Stephanie Seminara Yu-Zhu Cheng Wei-Ping Li Gavin Maccoll Anna V Eliseenkova Shaun K Olsen Omar A Ibrahimi Frances J Hayes Paul Boepple Janet E Hall Pierre Bouloux Moosa Mohammadi William Crowley

Idiopathic hypogonadotropic hypogonadism (IHH) due to defects of gonadotropin-releasing hormone (GnRH) secretion and/or action is a developmental disorder of sexual maturation. To date, several single-gene defects have been implicated in the pathogenesis of IHH. However, significant inter- and intrafamilial variability and apparent incomplete penetrance in familial cases of IHH are difficult to...

2014
BŁAŻEJ MĘCZEKALSKI AGNIESZKA PODFIGURNA-STOPA ADAM CZYŻYK KRZYSZTOF KATULSKI MARZENA MACIEJEWSKA-JESKE

Hypoestrogenism is referred to lower than normal serum levels of estrogen. Hypoestrogenism can be regarded as typical and physiological in postmenopausal women. However, hypoestrogenism which oocurs in young women is related to pathological background. There are two groups of disorders in young women related to hypoestrogenism: hypogonadotropic hypogonadism and hypergonadotropic hypogonadism. H...

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