نتایج جستجو برای: biliary atresia

تعداد نتایج: 37266  

Journal: :Nuklearmedizin. Nuclear medicine 2009
Ramin Sadeghi Hamid Reza Kianifar Vahid Reza Kakhki Seyyed Rasoul Zakavi Kianoush Ansari

AIM Hepatobiliary scintigraphy is an integral part in the diagnostic work-up of the neonatal cholestasis syndrome. However, less than optimal specificity is its major disadvantage. Differentiation between biliary atresia and neonatal hepatitis is nearly impossible in some cases with poor hepatocellular function. 99mTc sestamibi (MIBI) is a cationic lipophilic agent which is a substrate of P-gly...

2017
Junbae Jee Reena Mourya Pranavkumar Shivakumar Lin Fei Michael Wagner Jorge A Bezerra

Biliary atresia is progressive fibro-inflammatory cholangiopathy of young children. Central to pathogenic mechanisms of injury is the tissue targeting by the innate and adaptive immune cells. Among these cells, neutrophils and the IL-8/Cxcl-8 signaling via its Cxcr2 receptor have been linked to bile duct injury. Here, we aimed to investigate whether the intestinal microbiome modulates Cxcr2-dep...

Journal: :The Journal of clinical investigation 2014
Jun Li Nataliya Razumilava Gregory J Gores Stephanie Walters Tatsuki Mizuochi Reena Mourya Kazuhiko Bessho Yui-Hsi Wang Shannon S Glaser Pranavkumar Shivakumar Jorge A Bezerra

Injury to the biliary epithelium triggers inflammation and fibrosis, which can result in severe liver diseases and may progress to malignancy. Development of a type 1 immune response has been linked to biliary injury pathogenesis; however, a subset of patients with biliary atresia, the most common childhood cholangiopathy, exhibit increased levels of Th2-promoting cytokines. The relationship am...

Journal: :Arquivos de gastroenterologia 2014
Thais Costa Nascentes Queiroz Alexandre Rodrigues Ferreira Eleonora Druve Tavares Fagundes Mariza Leitão Valadares Roquete Francisco José Penna

CONTEXT Biliary atresia is a progressive, idiopathic, fibro-obliterative disease of the extrahepatic biliary tree that presents with biliary obstruction exclusively in the neonatal period. OBJECTIVES To assess the differences regarding age at referral, age at surgery, duration of propaedeutics and waiting time for surgery between two groups of infants in different periods. METHODS Retrospec...

2014
Liesbeth Claire Faverey Yvan Vandenplas

A 4-week-old infant presented with a coagulation disorder resulting from a vitamin K deficiency. The vitamin K deficiency was caused by neonatal cholestasis due to biliary atresia. Jaundice, hepatomegaly and pale stools are the predominant presenting symptoms of biliary atresia, none of which were recognized in our patient before admission. However, the patient presented with bleeding caused by...

Journal: :Archives of disease in childhood 1994
M S Fewtrell G Noble-Jamieson S Revell J Valente P Friend P Johnston A Rasmussen N Jamieson R Y Calne N D Barnes

UNLABELLED One hundred and seventy three children, including 93 with biliary atresia, received liver grafts at Addenbrooke's Hospital between 1983 and 1993. Of these, only seven developed cyanosis due to intrapulmonary shunting as a complication of their liver disease, and all seven of these had the biliary atresia/polysplenia syndrome. Intrapulmonary shunting was confirmed by a radioisotope sc...

Journal: :The Journal of infectious diseases 1996
M Riepenhoff-Talty V Gouvea M J Evans L Svensson E Hoffenberg R J Sokol I Uhnoo S J Greenberg K Schäkel G Zhaori J Fitzgerald S Chong M el-Yousef A Nemeth M Brown D Piccoli J Hyams D Ruffin T Rossi

The purpose of this retrospective study was to examine liver tissue from patients with cholestatic disease for the presence of group C rotavirus RNA. The reverse transcriptase-polymerase chain reaction (PCR) for genes 5 and 6 was used, and the PCR products were subjected to liquid hybridization with a 32P-labeled probe. A second amplification with nested primers was also used. Samples from 32 s...

Journal: :British journal of anaesthesia 1995
A A Raoof L J van Obbergh R K Verbeeck

We studied the pharmacokinetics of an i.v. bolus dose of propofol 2.5-3.0 mg kg-1 in eight children (age 4-24 months) with biliary atresia and in six control (ASA I) children (age 11-43 months). Blood samples were obtained for 4 h after administration of propofol. Blood concentrations of propofol were measured by high pressure liquid chromatography. Systemic clearance of propofol (CI) and volum...

Journal: :Indian journal of gastroenterology : official journal of the Indian Society of Gastroenterology 2005
A S M Bazlul Karim M Kamal

BACKGROUND AND OBJECTIVE Cholestatic jaundice in early infancy is a difficult diagnostic problem. Early diagnosis is important for proper management. This retrospective study was conducted to find out the etiology and clinical profile of neonatal cholestatic disorders in Bangladesh. SETTING Tertiary-care hospital in a developing country. METHODS Clinical profile and cause of cholestatic ill...

Journal: :Expert review of gastroenterology & hepatology 2009
Toshihiro Muraji David L Suskind Naoki Irie

Biliary atresia is an idiopathic neonatal cholestatic disease characterized by the destruction of both the intra- and extra-hepatic biliary ducts. There are two clinical manifestations of the disease: an embryonal subtype, which often presents at birth and is associated with congenital malformations, and a 'perinatal' subtype, which is probably an acquired disease due to unknown etiology. Over ...

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