how to cite this article: fadakar k, dadkhahfar s, esmaeili a, keyhanidoust z. a case of schizencephaly and septo-optic dysplasia presenting with anterior encephalocele. iran j child neurol autumn 2012; 6(4):47-50.   abstract schizencephaly is a rare central nervous system disorder with variable presentations. here we report a patient with a huge bilateral schizencephaly and septo-optic dysplas...

698 March 2015 A full-term, 69-dayold infant with an antenatal diagnosis of a frontonasal encephalocele presented for a bifrontal craniotomy and encephalocele resection. The encephalocele measured 4.5 cm by 4.5 cm and extended from the patient’s glabella to his nasal alae. It was soft and covered with intact skin. The remainder of his airway examination (including computed tomography) was unrem...

BACKGROUND Intrasphenoidal encephaloceles are extremely rare findings. Sternberg's canal is a lateral craniopharyngeal canal resulting from incomplete fusion of the greater wings of the sphenoid bone with the basisphenoid. It acts as a weak spot of the skull base, which may lead to develop a temporal lobe encephalocele protruding into the lateral recess of the sphenoid sinus (SS). CASE DESCRI...

Encephalocele is a rare condition that consists of herniation of cerebral matter through openings of dura and skull. A majority of encephaloceles are congenital and manifest in childhood. We present a case of a 45-year-old man presenting with contralateral hemiparesis and found to have an extremely rare phenomenon of a symptomatic posttraumatic parietal intradiploic encephalocele (IE) manifesti...

Glial choristomas are isolated masses of mature brain tissue that are found outside the spinal cord or cranial cavity. These masses are rare, especially in the middle ear. We describe the case of an 81-year-old man who presented with left-sided chronic otitis media, mastoiditis, hearing loss, tinnitus, and aural fullness. He was found to have a glial choristoma of the middle ear on the left. Ot...

Background Recurrent bacterial meningitis in children poses a considerable diagnostic challenge due to its multiple etiologies. Making an early diagnosis is crucial in preventing further episodes that could lead to a potentially life threatening condition, neurologic sequelae and psychological trauma due to multiple invasive investigations. Recurrent bacterial meningitis has multiple underlying...

A 45-year-old woman had complex partial seizures for 25 years with pharmacoresistance for 2 years. EEG showed right temporal epileptiform discharges. MRI revealed atrophy of the right temporal parenchyma (figure, A) herniating toward the pterygomaxillary fossa and the sphenoidal sinus (figure, C). CT demonstrated the bone defect of the sphenoid wing (figure, B) whereas the fusion of both techni...