The current authors retrospectively assessed 56 hip shelf arthroplasties (48 patients) with a mean followup of 17 years (range, 15-30 years) and 89 Chiari osteotomies (82 patients) with a mean followup of 13 years (range, 6-25 years) done in adults with painful hip dysplasia. Preoperative joint space narrowing was observed in 32 of 56 shelf arthroplasties and in 67 of 89 Chiari osteotomies. Sur...

In this report, we describe a case of pyrrolizidine alkaloid-related Budd-Chiari syndrome in Hong Kong. A 10-month-old boy presented with ascites, right pleural effusion, and hepatomegaly after consumption of herbal drinks for 3 months. His clinical (including imaging) features were compatible with Budd-Chiari syndrome. Budd-Chiari syndrome is a rare disease entity in paediatric patients. In ou...

BACKGROUND Chiari II deformity is associated with open spinal dysraphism. A causal relationship has been proposed by McLone and Knepper. This article evaluates that hypothesis. OBJECTIVE To establish the frequency of Chiari II deformity in fetuses with open spinal dysraphism, assess whether meningocele sac neck area and volume influence the severity of posterior fossa changes, and assess whet...

A retrospective study was performed that analyzed 23 patients who had an orthotopic liver transplantation for the Budd-Chiari syndrome with end-stage liver disease. Patient follow-up was as long as 14 years. The technical considerations relevant to the Budd-Chiari syndrome were discussed. There have been no serious complications of postoperative anticoagulation. Three patients, all of whom died...

INTRODUCTION The risk that patients with Behçet's disease will develop thrombotic complications has been previously described. Although it is distributed worldwide, Behçet's disease is rare in the Americas and Europe. Even though the pathogenic mechanisms of vascular complications of Budd-Chiari syndrome in patients with Behçet's disease are unknown, severe vascular complications of Budd-Chiari...

804 Chiari malformations are a heterogeneous group of congenital disorders that are defined by anatomic anomalies of the cerebellum, brainstem, and craniocervical junction, with downward displacement of the cerebellum, either alone or together with the lower medulla, into the spinal canal. 1 The major categories of symptoms of Chiari malformations are those related to obstructive hydrocephalus,...

OBJECTIVE The aim of this study was to determine the posterior cranial fossa volume, cerebellar volume, and herniated tonsillar volume in patients with chiari type I malformation and control subjects using stereological methods. MATERIAL AND METHODS These volumes were estimated retrospectively using the Cavalieri principle as a point-counting technique. We used magnetic resonance images taken...

Tonsil motion was measured with cine MR imaging in patients clinically suspected of having Chiari I malformation. Cardiac-gated sagittal 2D fast imaging employing steady-state acquisition (2D FIESTA) was performed in 11 patients with a Chiari I malformation and in 6 subjects without tonsil ectopia. Tonsil motion was measured through the cardiac cycle with a pixel-shift program designed for that...

ABSTRACTThe valves of right horn of systemic venous sinus are prominent structures within the right atrium during early embryonic period. Involution of these structures may not be complete, resulting in a spectrum of anatomical presentations such as cyanosis. A full-term male neonate referred to our hospital for precise evaluation of severe cyanosis on the first day of life. Echocardiographic e...

BACKGROUND AND PURPOSE Upper cervical spinal canal dimension may have a role in abnormal CSF dynamics in patients with Chiari I malformation. We attempted to measure spinal canal tapering from anteroposterior spinal canal dimensions in patients with Chiari I. MATERIALS AND METHODS Twenty-one patients with Chiari I malformation, including 12 with syringomyelia and 7 patients with IS were ident...