Fahr's disease (FD) is characterized by sporadic or familiar idiopathic calcification of the basal ganglia, dentate nuclei of the cerebellum, and centrum semiovale, mainly presenting with movement disorder, dementia, and behavioral abnormalities. We described a rare case of Fahr's disease presenting at onset only with behavioral and neuropsychological alterations, whose diagnosis was supposed o...

1 Wisniewski KE, French JH, Rosen JF, Koslowski PB, Tenner M, Wisniewski HM. Basal ganglia calcification (BGC) in Down's syndrome. Another manifestation of premature aging. Ann NYAcad Sci 1982;396:179-89. 2 Jakab I. Basal ganglia calcification and psychosis in mongolism. Eur Neurol 1978;17:300-14. 3 Lowenthal A, De Deyn P. Striopallidodentate calcifications. In: Joseph AB, Young RR, eds. Moveme...

OBJECTIVE To report a case series in which basal ganglia calcifications without mass effect proved to be germ cell tumors. DESIGN Case series. SETTING Tertiary care hospital. PATIENTS Four patients. INTERVENTIONS Computed tomography, magnetic resonance imaging, positron emission tomography, biopsy, chemotherapy, and radiation therapy. MAIN OUTCOME MEASURES Recognition of clinical synd...

BACKGROUND Fahr's disease is a rare neurodegenerative disorder characterized by diffuse intracranial calcium deposition and associated cell loss mainly in bilateral basal ganglia and dentate nuclei of the cerebellum. Subarachnoid hemorrhage and epileptic syncope had been reported as acute presentation of Fahr's disease. We here report a 36-year-old male Indonesian diagnosed as Fahr's disease pr...

Fahr syndrome (FS) refers to basal ganglia calcification that is associated with many neurological and psychiatric abnormalities and appears as secondary to other diseases. We described a case of FS patient who was admitted in the Department of Neurology of "Prof. Dr. Nicolae Oblu" Clinical Emergency Hospital, Iassy, Romania, with seizure and mood disorders. On CT, the cause of seizure was foun...

Two cases (one female and one male) of Fahr's syndrome are reported here. Both of them had neuropsychiatric disturbances and intracranial calcifications in bilateral basal ganglia and cerebral hemispheres. CT scan helped in establishing the diagnosis. Both of them were treated with antipsychotic drugs and responded to some extent.

In 1860, Delacour was the first to report vascular calcifications in the basal ganglia in a male who presented rigidity, weakness in his lower limbs, and tremor.1 Although known as Fahr’s disease, this is a misnomer, since this latter author reported a case of calcinosis in the basal ganglia that does not correspond to what we currently understand this term to mean. Since the calcifications exh...

Aicardi-Goutieres syndrome is a familial progressive early onset encephalopathy with basal ganglia calcifications, chronic CSF lymphocytosis and high level of interferon-alpha in CSF. Cutaneous necrotic lesions and the neuropathological aspect of microangiopathy and microinfarctions suggest a vascular process in relation to elevated interferon-alpha. A genetic defect in the regulation of its sy...

Objective
 In this study, the anatomical localization and
 distribution of intracranial calcifications detected on
 brain computed tomography (CT) were determined
 and their relationship with age gender was
 investigated.
 Material Method
 Images 887 patients who underwent CT
 examinations for various reasons between March
 2010 May 2013 analyzed. 12...