Normal hepatic arterial anatomy occurs in approximately 50-80% of cases; for the remaining cases, multiple variations have been described. Knowledge of these anomalies is especially important in hepatobiliary and pancreatic surgery in order to avoid unnecessary complications. We describe two cases of patients undergoing pancreatoduodenectomy for abnormalities in the head of the pancreas. Preope...

Congenital anomalies in the origin, course or distribution of the epicardial coronary arteries are found in 1 to 2 percent of the population. Asymptomatic coronary artery anomalies are generally diagnosed incidentally by routine coronary angiography or during autopsy. Approximately 80% of congenital anomalies of the coronary arteries are benign, while 20% of coronary artery anomalies produce li...

The case of a 2-month-old female infant with PHACES syndrome is reported. PHACES represents a broad spectrum of congenital anomalies, including the following primary features: posterior fossa brain malformations, large facial hemangiomas, arterial anomalies, cardiac defects and aortic coarctation, eye abnormalities, and ventral developmental defects. The literature on this rare condition is rev...

CONTEXT Standard celiac and hepatic arterial anatomy occur in approximately 60% of the patients; for the remaining, multiple variations have been described. A thorough knowledge of these anomalies is important in order to avoid unnecessary complications. In this report we describe one of the rarest arterial anomalies, a hepatomesenteric trunk supplying the liver. We attempt to elucidate its imp...

INTRODUCTION Twin reversed arterial perfusion (TRAP) sequence is a rare complication of multiple pregnancy caused by defects in early embryogenesis. The pump twin supplies the acardiac recipient twin with blood, and although the pump twin is usually structurally normal, congenital anomalies have sometimes been reported. We report a unique case of twin reversed arterial perfusion sequence with a...

PURPOSE To assess the potential of magnetic resonance angiography (MRA) as an adjunct to spin-echo sequences in evaluating the cerebral vascular anomalies seen in Sturge-Weber syndrome. METHODS Four pediatric patients with Sturge-Weber syndrome were evaluated with conventional MR imaging and with arterial and venous MRA. Resultant images were evaluated for evidence of volume loss, cortical en...

Coronary anomalies comprise a diverse group of malformations, some of them asymptomatic with a benign course, and the others related to symptoms as chest pain and sudden death. Such anomalies may be classified as follows: 1) anomalies of origination and course; 2) anomalies of intrinsic coronary arterial anatomy; 3) anomalies of coronary termination. The origin and the proximal course of anomal...

twin reversed arterial perfusion (trap) sequence is a syndrome with poor prognosis, seen only in monochorionic monozygotic twin pregnancies. the incidence is one in 35.000 births and one in 100 monozygotic twin pregnancies. it is characterized with a recipient fetus exhibiting lethal anomalies including acardia and a pump fetus. mortality is usually due to heart failure or premature labor cause...

A nomenclature is described for congenital heart disease employing sequential chamber localization. It is an eclectic system based in part upon the previous classifications of Van Praagh and Kirklin. It links together the atrial, ventricular, and arterial segments of the heart and then permits tabulation of associated anomalies. The atrial segment of the heart can exist as situs solitus, situs ...

Abstract According to the International Society for Study of Vascular Anomalies (ISSVA) classification, vascular anomalies include a diverse range pathologies, classified as either tumors or malformations. This last revised in 2018, aims explain biological basis lesions and help clinicians manage anomalies. In tumors, there are proliferative changes endothelial cells, while malformations primar...