نتایج جستجو برای: small supernumerary marker chromosome ssmc

تعداد نتایج: 1015567  

Small supernumerary marker chromosomes (sSMC) are still a major problem in clinical cytogenetics as they cannot be identified or characterized unambiguously by conventional cytogenetics alone. On the other hand, and perhaps more importantly in prenatal settings, there is a challenging situation for counseling how to predict the risk for an abnormal phenotype, especially in cases with a de novo ...

Journal: :Cytogenetic and genome research 2012
E Klein M Rocchi A Ovens-Raeder N Kosyakova A Weise M Ziegler M Meins S Morlot W Fischer M Volleth A Polityko C Mackie Ogilvie C Kraus T Liehr

Since the first report in 1993, an ectopic centromere, i.e. neocentromere formation, has been reported in more than 100 small supernumerary marker chromosomes (sSMC), in 7 instances of centromere repositioning, and in about a dozen cases with more complex chromosomal rearrangements. Here we report 2 new cases with centromere repositioning and 3 neocentric sSMC consisting exclusively of heteroch...

Journal: :European journal of medical genetics 2005
Thomas Liehr Elke Brude Gabriele Gillessen-Kaesbach Rainer König Kristin Mrasek Ferdinand von Eggeling Heike Starke

Prader-Willi (PWS) and Angelman (AS) are syndromes of developmental impairment that can result either from a 15q11-q13 deletion, paternal uniparental disomy (UPD), imprinting, or UBE3A mutations. A small cytogenetic subset of PWS and AS patients are carriers of a so-called small supernumerary marker chromosome (sSMC). Here, we report on an previously unreported PWS case with a karyotype 47,XY,+...

Journal: :Journal of the Chinese Medical Association : JCMA 2010
Thomas Liehr Rolf-Dieter Wegner Markus Stumm Thomas Martin Gabriele Gillessen-Kaesbach Nadezda Kosyakova Elisabeth Ewers Ahmed Basheer Hamid Ferdinand von Eggeling Julia Hentschel Monika Ziegler Anja Weise

Small supernumerary marker chromosomes (sSMCs) are a major problem in prenatal cytogenetic diagnostics. Over two-thirds of cases carrying an sSMC derived from chromosome 1 are associated with clinical abnormalities. We report 3 further cases of such sSMCs that did not show any clinical abnormalities. All 3 sSMCs studied were detected prenatally and characterized comprehensively for their geneti...

Journal: :Cytogenetic and genome research 2004
T Liehr U Claussen H Starke

Small supernumerary marker chromosomes (sSMC), defined as additional centric chromosome fragments too small to be identified or characterized unambiguously by banding cytogenetics alone, are present in 0.043% of newborn children. Several attempts have been made to correlate certain sSMC with a specific clinical picture, resulting in the description of several syndromes such as the i(18p)-, der(...

Journal: :American journal of medical genetics. Part A 2006
Thomas Liehr Heike Starke Gabriele Senger Cindy Melotte Anja Weise Joris Robert Vermeesch

Small supernumerary marker chromosomes (sSMC) in human are defined as additional centric derivatives smaller than chromosome 20. In the majority of the cases only one sSMC is present, leading to a more or less stable karyotype of 47,XX,+mar or 47,XY,+mar. In approximately 1.4% of sSMC cases two or up to seven markers of different chromosomal origin are reported. According to the literature a sS...

Journal: :The journal of histochemistry and cytochemistry : official journal of the Histochemistry Society 2007
Holger Tönnies Joanna Pietrzak Ewa Bocian Kay MacDermont Alma Kuechler Britta Belitz Udo Trautmann Angela Schmidt Berndt Schulze Laura Rodríguez Franz Binkert Catharine Yardin Nadezda Kosyakova Marianne Volleth Hasmik Mkrtchyan Isolde Schreyer Ferdinand von Eggeling Anja Weise Kristin Mrasek Thomas Liehr

Sixteen newly established cell lines with small supernumerary marker chromosomes (sSMC) derived from chromosomes 1, 2, 4, 6, 7, 8, 14, 15, 16, 18, 19, 21, and 22 are reported. Two sSMC are neocentric and derived from 15q24.1-qter and 2q35-q36, respectively. Two further cases each present with two sSMC of different chromosomal origin. sSMC were characterized by multicolor fluorescence in situ hy...

Journal: :Molecular Cytogenetics 2021

Abstract Background Non-invasive prenatal testing (NIPT) is a rapidly developing and widely used method in the screening. Recently, widespread use of NIPT caused neglecting limitations this technology. Case presentation The 38-year-old woman underwent amniocentesis because high risk trisomy 2 revealed by genome-wide Non-Invasive Prenatal Test (NIPT). invasive diagnosis mosaicism for small super...

Journal: :European journal of medical genetics 2011
Frenny Sheth Joris Andrieux Elisabeth Ewers Nadezda Kosyakova Anja Weise Harsh Sheth Serge-Pierrick Romana Marc LeLorc'h Bruno Delobel Olivier Theisen Thomas Liehr Sheela Nampoothiri Jayesh Sheth

Small supernumerary marker chromosome (sSMC) is a structurally altered additional chromosome that may not be explicitly clarified by conventional karyotyping alone. About one third of sSMC carriers have abnormal phenotypes and its clinical correlation is difficult, especially in prenatal studies. The present study was aimed at characterizing 19 sSMC identified in 15 patients with dysmorphic fea...

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