Hepatopulmonary syndrome (HPS) and portopulmonary hypertension (PPHTN) are the two major pulmonary vascular complications of liver disease. While HPS is characterized by low pulmonary vascular resistance, PPHTN is defined by the presence of elevated pulmonary vascular resistance. Given these seemingly opposing pathophysiologic mechanisms, these conditions were traditionally felt to be mutually ...

INTRODUCTION Hepatopulmonary syndrome is a rare disease that affects patients of any age with acute or chronic liver disease. Liver transplantation is the only therapeutic option of proved benefit, and can result in substantial improvement or total improvement in postoperative gas exchange abnormalities. CASE PRESENTATION We report the case of a cyanotic 13-year-old Pakistani boy whose chest ...

background : hepatopulmonary syndrome (hps) refers to arterial hypoxemia caused by pulmonary vasodilation, which is a consequence of portal hypertension. hps is associated with increased morbidity and mortality; thus, it is important to diagnose this entity as soon as possible for treatment to be administered. materials and methods: in a cross-sectional study, 40 children (6 months to 14 years ...

We report the case of a 17-year-old male with Marfanoid habitus who presented with deep cyanosis, haematemesis, dyspnoea and platypnoea. He had oesophageal varices, indicating portal hypertension, with mildly deranged liver function. His arterial blood gas (ABG) revealed hypoxia and orthodeoxia. Contrast-enhanced echocardiography with agitated saline and a 99m Technetium macro-aggregated albumi...