نتایج جستجو برای: shprintzen syndrome

تعداد نتایج: 621913  

2003
D. IVANOV G. KIROV H. J. WILLIAMS N. M. WILLIAMS I. NIKOLOV R. TZWETKOVA S. M. STAMBOLOVA K. C. MURPHY D. TONCHEVA A. THAPAR M. C. O ’ DONOVAN J. OWEN

Declaration of interest Funding fromthe PPPHealthcare Medical Trust, London,UK.Collection of probands in Bulgaria fundedby the Janssen Research Foundation and inthe UK by the Medical Research Council. Velo-cardio-facial syndrome (VCFS) is a genetic disorder associated with characteristic dysmorphology, cleft palate, cardiac anomalies and major psychiatric disorders, including schizophrenia (Shp...

Journal: :Current Biology 2016
Josta T. Kevenaar Sarah Bianchi Myrrhe van Spronsen Natacha Olieric Joanna Lipka Cátia P. Frias Marina Mikhaylova Martin Harterink Nanda Keijzer Phebe S. Wulf Manuel Hilbert Lukas C. Kapitein Esther de Graaff Anna Ahkmanova Michel O. Steinmetz Casper C. Hoogenraad

Kinesin motor proteins play a fundamental role for normal neuronal development by controlling intracellular cargo transport and microtubule (MT) cytoskeleton organization. Regulating kinesin activity is important to ensure their proper functioning, and their misregulation often leads to severe human neurological disorders. Homozygous nonsense mutations in kinesin-binding protein (KBP)/KIAA1279 ...

2013
Ahmed Abdelmeged

We are after a Wikipedia for formal scientific knowledge; a crowdsourcing system where formal science claims are expressed as interpreted logical statements (a.k.a. claims). The crowd takes positions on claims and objectively argues these positions through Semantic Games (SGs). SGs are zero-sum, two-person games where players take two contradictory positions on claims and exchange examples and ...

Journal: :American journal on intellectual and developmental disabilities 2014
Ling M Wong Tracy Riggins Danielle Harvey Margarita Cabaral Tony J Simon

Individuals with chromosome 22q11.2 deletion syndrome (22q11.2DS) have been shown to have impairments in processing spatiotemporal information. The authors examined whether children with 22q11.2DS exhibit impairments in spatial working memory performance due to these weaknesses, even when controlling for maintenance of attention. Children with 22q11.2DS (n  =  47) and typically developing contr...

Journal: :Neuroscience 2009
E Walter P K Mazaika A L Reiss

Over the past few decades, behavioral, neuroimaging and molecular studies of neurogenetic conditions, such as Williams, fragile X, Turner and velocardiofacial (22q11.2 deletion) syndromes, have led to important insights regarding brain development. These investigations allow researchers to examine "experiments of nature" in which the deletion or alteration of one gene or a contiguous set of gen...

Journal: :American journal of medical genetics. Part A 2006
Abee L Boyles David S Enterline Preston H Hammock Deborah G Siegel Susan H Slifer Lorraine Mehltretter John R Gilbert Diane Hu-Lince Dietrich Stephan Ulrich Batzdorf Edward Benzel Richard Ellenbogen Barth A Green Roger Kula Arnold Menezes Diane Mueller John J Oro' Bermans J Iskandar Timothy M George Thomas H Milhorat Marcy C Speer

Chiari type I malformation (CMI; OMIM 118420) is narrowly defined when the tonsils of the cerebellum extend below the foramen magnum, leading to a variety of neurological symptoms. It is widely thought that a small posterior fossa (PF) volume, relative to the total cranial volume leads to a cramped cerebellum and herniation of the tonsils into the top of the spinal column. In a collection of ma...

پایان نامه :دانشگاه آزاد اسلامی واحد علوم پزشکی تهران - دانشکده پزشکی 1390

مقدمه : impingement syndrome یکی از بیماریهای شایع است که با درد شانه ومحدودیت حرکت در مفصل شانه همراه می باشد. با توجه به اهمیت این موضوع و لزوم دستیابی به روشی مطمئن جهت درمان مبتلایان به این بیماری، در این مطالعه به بررسی میزان اثربخشی استفاده از glyceril trinitrate بصورت موضعی در درمان مبتلایان بهimpingement syndrome پرداختیم. مواد و روشها: در این مطالعه که از نوع مداخله ای-تحلیلی میباشد60...

2017
Ali Al Kaissi Zahra Marrakchi Nabil M. Nassib Jochen Hofstaetter Franz Grill Rudolf Ganger Susanne Gerit Kircher

RATIONALE Craniosynostosis is a disorder characterized by premature fusion of cranial sutures with subsequent development of abnormal craniofacial contour associated with variable skeletal and extra-skeletal abnormalities. In this family syndromic type of craniosynostosis was recognized and the etiology behind diverse forms of deformities have been diagnosed. PATIENT CONCERNS The negative imp...

2009

● Primary care physicians may encounter situations in which a genetic diagnosis is now possible in an individual with developmental delay whose previous genetic workup was negative. ● Testing for small chromosomal deletions, such as 22q11.2 deletion syndrome, represents an example of the improved diagnostic capabilities of current genetic testing. ● 22q11.2 deletion syndrome includes a range of...

پایان نامه :وزارت بهداشت، درمان و آموزش پزشکی - دانشگاه علوم پزشکی و خدمات بهداشتی درمانی استان فارس - دانشکده دندانپزشکی 1399

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