A patient with systemic lupus erythematosus was first diagnosed after she had developed the Budd-Chiari syndrome. We believe that the Budd-Chiari syndrome was part of her tendency for thrombosis, induced by the presence of a lupus anticoagulant. The association between enhanced thrombosis and the lupus anticoagulant is discussed, and the need for prompt recognition and administration of anticoa...

High-field-strength MR imaging was performed in one patient with Chiari III and 19 patients with Chiari II malformations. The MR features were compared with descriptions in the literature and correlated with previously described surgical and postmortem findings and with the results of previous radiologic investigations in this group of patients. Several new observations were apparent from the M...

CSF flow has been shown to exhibit complex patterns in MR images in both healthy subjects and in patients with Chiari I. Abnormal CSF flow oscillations, according to prevailing opinion, cause syringomyelia and other clinical manifestations that affect some patients with the Chiari I malformation. For this article, we reviewed the literature on PC MR of CSF flow, collected the published CFD stud...

Background: Chiari Malformation type 1 (CM-I) is a congenital disease characterized by downward decent of the cerebellar tonsil and crowding in the craniocervical junction area. There are still obvious controversies for the optimum surgical strategy for Chiari malformation type 1 especially if associated with syringomylia. Objectives: to determine the results of bony decompression with and with...

Transjugular intrahepatic portosystemic shunt (TIPS) is a new treatment modality in patients of intractable ascites with Budd-Chiari syndrome. We report a young lady who presented with intractable ascites and encephalopathy and diagnosed to have Budd-Chiari syndrome. She was treated with TIPS and on follow-up after 12 months she is free of ascites, encephalopathy and able to perform her daily w...

An enhancing nodule was seen on T1-weighted enhanced scans at the tip of the caudally displaced cerebellar vermis in three patients with Chiari II malformation. The enhancing fibrovascular nodule found at the base of the cerebellum in patients with Chiari II malformation represents ectopic choroid plexus and should not be confused with a pathologic mass.

background budd-chiari syndrome (bcs) is defined as hepatic venous outflow obstruction (hvoo). bcs is an uncommon, life-threatening liver disorder. this study describes the clinical and etiological characteristics in addition to the long-term outcome of bcs in a single referral center in tehran, iran. methods we reviewed long-term outcome of patients who were diagnosed with bcs between 1989 and...