نتایج جستجو برای: juvenile dermatomyositis

تعداد نتایج: 48304  

2014
Katherine L Green Marinka Twilt Taunton Southwood

Introduction Juvenile dermatomyositis is a rare autoimmune disease characterised by profound muscle weakness in addition to skin lesions, calcinosis, and underlying vasculopathy. Current treatment plans, including methotrexate and corticosteroids, are ineffective in some patients and may be associated with significant adverse events. The benefits and risks of etanercept in JDMS are not well stu...

2013
A Souto N Alvarez A Barros L Fernandez B Lopez I Calvo

Methods Patients diagnosed of Juvenile dermatomyositis in La Fe Hospital (Valencia, Spain) since June 1992 to March 2013. Dates are shown in median and interquartile range for non-parametric variables, and for parametric variables is given as mean and standard deviation. To assess response to treatment, we used Wilcoxon test for paired measures of non-parametric variables and t-student for para...

Journal: :The Journal of pediatrics 2005
Sampath Prahalad John F Bohnsack Christopher G Maloney Kevin O Leslie

Acute fibrinous and organizing pneumonia, a recently described form of diffuse acute lung injury, sometimes affects adults with inflammatory myopathy. We describe a child with juvenile dermatomyositis who had development of acute fibrinous and organizing pneumonia. There does not appear to be a successful method of treatment, particularly in severe cases with respiratory failure.

2013
I Pagnini G Simonini T Giani L Cantarini R Cimaz

Introduction Juvenile Dermatomyositis (JDM) is an inflammatory myopathy with a predilection for proximal muscles and skin. Current treatment of JDM includes early aggressive use of corticosteroids coupled with immunosuppressive drugs such as methotrexate, cyclosporine and intravenous immune globulins (IVIG). Delay to diagnosis and inadequate treatment increase the risk of developing calcinosis....

2017
Marlous L Grijsen Deborah Mchaile Inge Geut Raimos Olomi Maitseo Nwako Luis Requena William P Howlett Daudi R Mavura Marieke C J Dekker

To our knowledge, this is the first case report of juvenile dermatomyositis (JDM) in Tanzania. It demonstrates that the characteristic cutaneous findings of JDM may easily be overlooked, especially on dark skin, and the difficulty of clinical management in resource-constrained settings.

2013
C Ferrari GC Varnier A Consolaro D Marafon C Pilkington S Maillard M Jelusic-Drazic A Civino A Martini A Ravelli

Introduction Juvenile dermatomyositis (JDM) is a multisystem vasculopathic disease that affects primarily the skin and muscle and is characterized by high risk of morbidity and long-term damage. Regular patient assessment through standardized quantitative clinical measures is important to monitor the disease course over time and to evaluate treatment effectiveness. However, only a few outcome m...

2014
Felicitas Bellutti Enders Brigitte Bader-Meunier Eileen Baildam Tamas Constantin Pavla Dolezalova Brian Feldman Pekka Lahdenne Bo Magnusson Kiran Nistala Clarissa Pilkington Angelo Ravelli Ricardo Russo Marco van Brussel JanJaap van der Net Lucy Wedderburn Bas Vastert Nico Wulffraat Liza McCann Annet van Royen-Kerkhof

SHARE – workpackage 5: evidence based recommendations for diagnosis and treatment of juvenile dermatomyositis Felicitas Bellutti Enders, Brigitte Bader-Meunier, Eileen Baildam, Tamas Constantin, Pavla Dolezalova, Brian Feldman, Pekka Lahdenne, Bo Magnusson, Kiran Nistala, Clarissa Pilkington, Angelo Ravelli, Ricardo Russo, Marco van Brussel, JanJaap van der Net, Lucy Wedderburn, Bas Vastert, Ni...

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