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Abstract Research on synthesis of PVDF-SiO 2 nanofiber membrane by electrospinning multi-jet vertical method conveyor collector as a lithium-ion battery separator was systematically investigated. Various voltages 15 kV, 16 and 17 kV types PVDF such Aldrich, Solvay, both mixtures were used for synthesis. The synthesized 4 hours with distance between the tip needle, 10 cm, flow rate 2.6 mL/hour s...

1. Derry JMJ, Ochs HD, Francke U: Isolation of a novel gene mutated in Wiskott-Aldrich syndrome. Cell 78:635, 1994 2. Schwarz K, Nonoyama S, Peitsch MC, de Saint Basile G, Espanol T, Fasth A, Fischer A, Freitag K, Friedrich W, Fugmann S, Hossle H-P, Jones A, Kinnon C, Meindl A, Notarangelo LD, Wechsler A, Weiss M, Ochs HD: WASPbase: A database of WASand XLT-causing mutations. Immunol Today 17:4...

The Wiskott-Aldrich Syndrome (WAS) is an X-linked immunodeficiency condition characterized by microthrombocytopenia, eczema and recurrent infections. It is caused by mutations in the Wiskott-Aldrich Syndrome protein (WASP) gene. We investigated two Malay boys who presented with congenital thrombocytopenia, eczema and recurrent infections. Here we report two cases of WASP mutation in Malaysia fr...

The Wiskott-Aldrich syndrome protein (WASp) is a key regulator of actin polymerization in hematopoietic cells. The dynamic nature of cytoskeletal changes during a variety of cellular processes demands complex mechanisms for coordinated integration of input signals, precise localization within the cell, and regulated activation of the Arp2/3 complex. Mutations in the Wiskott-Aldrich syndrome gen...

Faculty of Health, University of Newcastle, Newcastle, NSW. Rosemary Aldrich, BA (Comm), MPH, FAFPHM, Public Health Physician and Conjoint Lecturer. Correspondence: Dr Rosemary Aldrich, Faculty of Health, University of Newcastle, PO Box 664J, Newcastle, NSW 2300. [email protected] The Medical Journal of Australia ISSN: 0025729X 6/20 December 2004 181 11/12 675-676 ©The Medical J...

A 24 year old male who suffered from the Wiskott-Aldrich syndrome developed intra-abdominal bleeding on two occasions. Radiological investigations showed aneurysmal dilatation of branches of the hepatic and superior mesenteric arteries. The second abdominal bleed necessitated laparotomy and the bleeding was localised to the kidneys. Right nephrectomy was performed and histological examination s...

The genus Liancalus Loew is revised for the Nearctic Region. Seven species are documented from this region including two new species: Liancalusgenualis Loew, Liancalushydrophilus Aldrich, Liancaluslimbatus Van Duzee, Liancaluspterodactyl sp. n., Liancalusquerulus Osten Sacken, Liancalussimilis Aldrich, and Liancalussonorus sp. n. Lectotypes are designated for the following species: Liancalusgen...

Evans, D. I. K., and Holzel, A. (1970). Archives of Disease in Childhood, 45, 527. Immune deficiency state in a girl with eczema and low serum IgM. Possible female variant of Wiskott-Aldrich syndrome. This report concerns an immune deficiency disorder in a girl with eczema. She has had recurrent infections including three severe attacks of herpes simplex and five attacks of pneumococcal meningi...

Carbomer gel was prepared with 300mM D-sorbitol (Sigma-Aldrich, St. Louis, MO) and 10mM HEPES free acid (Sigma-Aldrich, St. Louis, MO) in heated distilled water. A gelling agent, carbomer 940 (Snowdrift Farm, Tucson, AZ), was added to the heated sorbitol solution under constant stirring, to reach a concentration of 0.3%, based on a weight percent. Once the carbomer was completely dissolved in t...