Rachischisis and Anencephaly

SUMMARY Antenatal ultrasonography has an important rule in diagnosis of congenital malformation. At present identification of most major congenital abnormality during pregnancy depends on . sensitivity and resolution of the instrument, skilful and experienced sonologist and gestational age. Cranial and spinal defects and other malformations can be ferquently diagnosed with ultrasound. Major anomalies of Nervous and urogenital system include 50% Malformation perinataly and their incidence will increase in presence of musculoskeletal and cardiac anomaly. This is a report of a rare case with rachischisis and Anencephaly which has been diagnosed with ultrasonography Antenataly.