Successful Surgical Treatment for Vaginal Agenesis: Report of Two Cases of Mayer–Rokitansky–Küster–Hauser (MRKH) Syndrome

Authors

  • Mardi, Parham Student Research Committee, Alborz University of Medical Sciences, Karaj, Iran
Abstract:

Introduction: Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome is a rare disorder in women which identified as agenesis of vagina and hypoplasia or agenesis of uterine. Case presentation: in this study, two female cases (17, and 19 years old) diagnosed with MRKH (first one type 2, and second one type 1) are described. Both patients were presented with amenorrhea, and absence of vagina orifice. One of the patients also had abdominal pain. MRI and sonography revealed agenesis of vagina and hypoplasia of uterine in first patient and agenesis of vagina and uterine in second patient. Both patients underwent creation of neovagina using sigmoid colon. Conclusion: intestinal vaginoplasty using sigmoid colon could be a suitable choice for replacement of vagina in vaginal agenesis patients.

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Journal title

volume 10  issue 1

pages  1- 5

publication date 2021-01

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