Primary kaposiform hemangioendothelioma of ulna

Kaposiform hemangioendothelioma of paranasal sinus.

Kapossiform hemangioendothelioma (KHE) of the paranasal sins (PNS) is a rare cause of recurrent epistaxis. To date, only two cases of PNS KHE have been reported in the literature, both occurring in the pediatric population. The case presented here appears to be the first case of PNS KHE occurring in an adult. A 46-year-old white female presented with progressively worsening unilateral recurrent...

Infantile hemangioma or kaposiform hemangioendothelioma?

We read with interest the letter sent by Yoon et al (1) about transarterial embolization of a cervicofacial hemangioma associated with Kasabach–Merritt (KM) syndrome in a premature neonate. There are some facets of the letter that warrant further comments, namely the association of the KM phenomenon with vascular tumors and the use of proper consensus-approved terminology adopted by the Interna...

Pancreatic Kaposiform Hemangioendothelioma Not Responding to Sirolimus

Background  Kaposiform hemangioendothelioma (KHE) is a vascular tumor frequently associated with Kasabach-Merritt phenomenon (KMP), characterized by severe thrombocytopenia and consumptive coagulopathy. Visceral involvement in KHE is rare. In our recent experience, sirolimus has shown to be an effective treatment in cutaneous KHE, becoming indeed the treatment of choice in KMP. We report a case...

Kaposiform hemangioendothelioma: case report and literature review.

We report the identification of a kaposiform hemangioendothelioma (KH) in the oropharynx of a 3-year-old boy. This is a rare endothelial-derived spindle cell neoplasm affecting children and early adolescents with features common to capillary hemangioma and Kaposi sarcoma. Nine cases of head and neck KH have been reported, this being the first in the otolaryngology literature. Our patient underw...

Kaposiform hemangioendothelioma arising from the internal auditory canal.

Kaposiform hemangioendothelioma is a rare vascular tumor and locally aggressive endothelial-derived spindle cell neoplasm, which occurs almost exclusively in infants and adolescents. Radiologically, hemangioendothelioma, including Kaposiform hemangioendothelioma, is seen as a highly vascularized well-enhancing tumor, but no characteristic findings differentiate Kaposiform hemangioendothelioma f...

Kaposiform Hemangioendothelioma in a Newborn with Kasabach-Merritt Syndrome