Erythema annulare centrifugum: association with autoimmune polyglandular syndrome type 1
Authors
Abstract:
Autoimmune polyendocrine syndromes are a heterogeneousgroup of rare diseases characterized by autoimmune activityagainst more than one endocrine organ, although non-endocrineorgans can also be affected. We report the association of APS Iwith erythema annulare centrifugum in an 18-years-old male whopresented with multiple figurate erythema spreading on his trunkand extremities along with a history of multiple endocrine disorderssuch as diabetes mellitus, hypothyroidism, hypoparathyroidism,hypogonadism, and adrenal insufficiency from one year ago. Toour knowledge this is a very rare association.
similar resources
Erythema annulare centrifugum during rituximab treatment for autoimmune haemolytic anaemia.
References 1 Parsi K, Kossard S. Multiple hereditary glomangiomas: successful treatment with sclerotherapy. Australas J Dermatol 2002; 43: 43–47. 2 Goldman MP, Sadick NS, Weiss RA. Cutaneous necrosis, telangiectatic matting, and hyperpigmentation following sclerotherapy. Etiology, prevention, and treatment. Dermatol Surg 1995; 21: 19–29. 3 H elou J, Maatouk I, Moutran R, Wehb e J, Stephan F, Ob...
full textErythema Annulare Centrifugum: A Rare Skin Finding of Autoimmune Hepatitis
Erythema annulare centrifugum is characterized by dermal perivascular lymphocytic infiltrates. It is often associated with infections, autoimmune or neoplastic diseases but in most cases the cause is unexplained. A case of erythema annulare centrifugum related to autoimmune hepatitis in a 24-year-old woman is described in this case report. Clinical response of the autoimmune hepatitis to a comb...
full textSquamous cell lung carcinoma presenting with erythema annulare centrifugum.
Erythema annulare centrifugum (EAC) is a permanent or migrating eruption characterized by annular, arcuate, or polycyclic erythematous lesions that expand to the periphery when the medial parts fade. Darier was the first to described it in 1916 (1,2). Defining the incidence and prevalence of EAC is difficult because the literature mostly consists of case reports and brief reviews. Although its ...
full textPolyglandular autoimmune syndrome type II.
The polyglandular autoimmune syndromes (PAS) comprise a wide spectrum of autoimmune disorders. There exist a juvenile (PAS I) and an adult type (PAS II). The nature of PAS has been based on the presence of lymphocyte infiltration in the affected gland, organ-specific antibodies in the serum, cellular immune defects and an association with the human leucocyte antigen (HLA) DR/DQ genes or immune ...
full textThe Vogt-Koyanagi-Harada syndrome: association with autoimmune polyglandular syndrome type 1.
We describe a young woman with primary adrenal insufficiency, hypoparathyroidism (autoimmune polyglandular syndrome type 1), Graves disease, vitiligo, and alopecia universalis. Five years after the diagnosis, she presented with recurrent ophthalmological and neurological disorders as features of Vogt-Koyanagi-Harada syndrome. A marked therapeutic response was noted on systemic high-dose cortico...
full textPolyglandular autoimmune syndrome-type I.
Polyglandular autoimmune syndrome type I is a rare disorder characterized by mucocutaneous candidiasis (MC), hypoparathyroidism (HP) and adrenal insufficiency , requiring regular follow up as the components of the syndrome appear at different age groups. We report a six and half year boy having this syndrome and presenting with MC, HP and ectodermal dystrophy.
full textMy Resources
Journal title
volume 16 issue 2
pages 73- 76
publication date 2013-04-01
By following a journal you will be notified via email when a new issue of this journal is published.
Hosted on Doprax cloud platform doprax.com
copyright © 2015-2023