Epidermolysis Bullosa Puriginosa: Report of a Case

Authors

  • Dabiri Shahriar
  • Meymandi Simin Shamsi
  • Shafiei Hamidreza
Abstract:

Epidermolysis Bullosa Puriginosa is a genetic mechanobullous disease characterized by pruritus, lichenified or nodular prurigo-like lesions, occasional trauma-induced blistering, excoriations, milia, nail dystrophy and albopapuloid lesions that appear at birth or later. Scarring and prurigo are most prominent on the shins. Herein, we report a case with a history of blisters since childhood followed by intensely pruritic lesions predominantly on the shins and dystrophy of the toenails, milia, excoriations and diffuse post-lesional hyper and hypopigmentation.

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Journal title

volume 13  issue 1

pages  20- 23

publication date 2010-04-01

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