Cystic Fibrosis Presenting with Severe Dehydration in an Otherwise Normal Infant

Authors

  • H Karamifar Department of Endocrinology, Shiraz University of Medical Sciences, Shiraz
  • M Haghighat Department of Pediatrics, Divisions of Gastroenterology, Shiraz University of Medical Sciences, Shiraz
Abstract:

A 4-month-old male infant was referred to our center with clinical signs and symptoms of severe dehydration without fever, diarrhea, vomiting, or respiratory symptoms. The patient had a history of two similar episodes at 1.5 and 2 months of age without any known underlying cause. In each attack the patient was hospitalized and improved with management of dehydration and electrolyte imbalance. The main abnormal laboratory findings on all admissions were: hypochloremic, hyponatremic, hypokalemic metabolic alkalosis. Sweat chloride was checked at all admissions, and was found to be highly abnormal at the last admission. 

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Journal title

volume 26  issue 3-4

pages  182- 184

publication date 2001-12-01

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