Case Report: Hallervorden–Spatz Syndrome with Seizures

Authors

  • Sunil Gothwal Department of Pediatrics, All India Institute of Medical Sciences, New Delhi, India.
  • Swati Nayan Department of Obstetrics and Gynecology, Sawai Man Singh Medical College, Jaipur, Rajasthan, India.
Abstract:

Hallervorden-Spatz syndrome is a disorder characterized by dystonia, parkinsonism, and iron accumulation in the brain. The disease is caused by mutations in gene encoding pantothenate kinase 2 (PANK2) and patients have pantothenate kinase-associated neurodegeneration. We present an 8-year-old boy with progressive muscle dystonia, neuroregression, frequent fall and multiple injury marks of different stages. Seizures are rare with PANK2. This child had seizure onset at 4 years of age and seizure free on valproate and levetricetam. The CT scan showed tiger eye appearance and mutations on PANK2 gene.

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Journal title

volume 7  issue 2

pages  165- 166

publication date 2016-04

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