Brooke-Spiegler Syndrome: a case report

Authors

  • Abadian Mohammad
  • Layegh Pouran
  • Sistani Nourieh Sharifi
Abstract:

Brooke-Spiegler syndrome is a rare autosomal recessive disease characterized by adnexal neoplasms, particularly trichoepithelioma, cylindroma, and occasionally spiradenoma, which usually develop in second to third decades of life. We report this syndrome in a 16-year-old woman with tumors on face and scalp.

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Journal title

volume 10  issue 2

pages  157- 161

publication date 2007-07-01

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