A Case Report of Phakomatosis Pigmentovascularis in a Patient with Discoid Lupus Erythematosus and Epidermal Naevus
Authors
Abstract:
We report phakomatosis pigmentovascularis (PPV) detected in a 40- year-old male characterized by the presence of a port-wine stain in the background of aberrant Mongolian spots covering the back, nevus of Ota, ocular melanosis, epidermal nevus and a scaly patch with the diagnosis of discoid lupus erytematosus. These associations have not been reported yet.
similar resources
Phakomatosis Pigmentovascularis: A case report
An eighteen-year old man is reported who had a large nevus spilus on the right side of his body with port wine stain on the anterior and posterior sides of his trunk without any systemic involvement. Considering the clinical signs and skin biopsy report of the patient, the diagnosis of phakomatosis pigmentovascularis type IIIa was made.
full textPyoderma gangrenosum in a patient with antiphospholipid antibody negative systemic lupus erythematosus: A case report
In any description of leg ulcers in systemic lupus erythematosus (SLE), pyoderma gangrenosum (PG) earns a mention at least for its being quite rare in such patients. The causative role of aPL (antiphospholipid antibody) in dermatological manifestations of SLE is undermined by the occurrence of PG in aPL negative SLE patients. To the best of our knowledge, there are only two reports of PG in aPL...
full textAcute monolateral proptosis and orbital myositis in a patient with discoid lupus erythematosus: a case report
INTRODUCTION Discoid lupus erythematosus may lead to significant orbital inflammation syndrome. Ocular manifestations related to discoid lupus erythematosus are uncommon and few cases of eye inflammation are reported. CASE PRESENTATION A 37-year-old Caucasian woman with 5-year history of discoid lupus erythematosus presented with exophthalmos, periorbital pain and blurred vision in her right ...
full textEpidermal urocanic acid in discoid lupus erythematosus.
Sir, Ultraviolet radiation (UVR) induces isomerization of transurocanic acid (UCA), a natural component of human skin, into cis-UCA, which has been shown to suppress both delayed hypersensitivity and contact hypersensitivity (1). An autoantigen-speci®c T-cell-mediated mechanism has been proposed in both chronic cutaneous lupus erythematosus, presenting mostly as discoid lupus erythematosus (DLE...
full textRefractory Angioedema in a Patient with Systemic Lupus Erythematosus
Angioedema secondary to C1 inhibitor deficiency has been rarely reported to be associated with systemic lupus erythematosus. A genetic defect of C1 inhibitor produces hereditary angioedema, which is usually presented with cutaneous painless edema, but edema of the genital area, gastrointestinal and laryngeal tracts have also been reported.In lupus patients, angioedema may be the result of an ac...
full textMy Resources
Journal title
volume 11 issue 1
pages 34- 37
publication date 2008-04-01
By following a journal you will be notified via email when a new issue of this journal is published.
Hosted on Doprax cloud platform doprax.com
copyright © 2015-2023