Rhabdomyomatous Mesenchymal Hamartoma Associated with Congenital Anomalies: Report of an Unusual Perineal Case
نویسندگان
چکیده
The ectopic occurrence of skeletal muscles in skin is an unusual condition. These lesions are named rhabdomyomatous mesenchymal hamartoma now. More accurately speaking, this entity should be called “cutaneous rhabdomyomatous choristoma” because the skeletal muscle is not a normal element in skin. We described a case occurring in perineal region associated with amniotic band syndrome, imperforate anus, and intestinal atresia. The association with gastrointestinal tract anomaly has not been reported previously. This unusual case is documented and compared to two other cases reported in this region. (Dermatol Sinica 26: 93-98, 2008)
منابع مشابه
[Rhabdomyomatous mesenchymal hamartoma].
Rhabdomyomatous mesenchymal hamartoma is a rare congenital lesion which consists of randomly arranged striated muscle fibers interspersed with mesenchymal elements. We describe the clinical and histopathological features of a rhabdomyomatous mesenchymal hamartoma in a one year-old patient presenting a bilobulated lesion in the mid-cervical line. No associated congenital malformations were obser...
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