Early Repolarisation Syndrome Associated to Brugada Syndrome Like
نویسندگان
چکیده
Recent studies have suggested an association between several channulopathy diseases. However, the mechanism remains unclear. The aim of this case was to demonstrate the relation between Brugada Syndrome (BrS) and Early Repolarization Syndrome (ERS). We presented herein a 46_year_old women with no familial history of sudden death. She was hospitalized for ventricular tachycardia with a lipothymia episode. We recorded in the electrophysiology study a fractionated electrogram in the same time with ventricular depolarization after fascicular electrograms. This fractionated electrograms precede slurring of the terminal portion of the R wave (J wave) and the atrial stimulation with extrastimulus decaled the fractionated electrograms responsible of Brugada Syndrome type 1 on the ECG. Brugada Syndrome (BrS) and Early Repolarization Syndrome (ERS) suggesting that two syndromes with J wave’s disorders have the same mechanism: wave front fragmentation in the anterolateral free wall of the RVOT responsible of ventricular tachycardia (VT).
منابع مشابه
A Review of the Mechanisms of Ventricular Arrhythmia in Brugada Syndrome
Brugada syndrome (BrS) is characterised by the triad of coved ST elevation, lethal ventricular arrhythmia in an apparently structurally normal heart. The precise mechanisms responsible for the coved ST elevation and ventricular arrhythmias in this disease have been debated since its initial description in 1992. Indeed the recent recognition of early repolarisation J wave disorders linked to pri...
متن کاملPerformance of electrophysiologic study in an asymptomatic patient with type 2 intermittent Brugada syndrome: To do or not to do?
Background: Brugada syndrome (BrS) is an inherited channelopathy, which is associated with sudden cardiac death due to rapid polymorphic VT or VF. There is no definite consensus regarding the management of asymptomatic patients. Some experts advocate close follow-up; others propose the programmed stimulation for risk stratification. We aimed to evaluate the benefit of complete atrial and ventri...
متن کاملBifid T waves induced by isoprenaline in a patient with Brugada syndrome.
A 41 year old man with incomplete right bundle branch block and persistent coved-type ST elevation in the right precordial leads during sinus rhythm had an episode of syncope while driving. He had never had syncope before and there was no family history of sudden cardiac death. Ventricular fibrillation was induced during electrophysiological study (EPS) by double extrastimuli applied to the rig...
متن کاملA case of Brugada Syndrome unmasked by a postoperative febrile state
Abstract Background: Brugada Syndrome (BS) is an inherited ion channelopathy characterized by an electrocardiographic (ECG) pattern of a coved type ST segment elevation in right precordial leads with or without right bundle branch block. Case Presentation: A 23-year old male presented with right lower quadrant abdominal pain. Further evaluation revealed a diagnosis of acute appendicitis. The ...
متن کاملThe management of Brugada syndrome patients.
Brugada syndrome is a congenital electrical disorder characterised by the appearance of distinctive QRST-T patterns in the right precordial leads and an increased risk of sudden death (SCD) in young healthy adults. Although chamber enlargement is not apparent in most cases, autopsy and histological investigations have revealed structural abnormalities. The typical Brugada ECG manifestation is o...
متن کامل