Thickness of the midventricular left ventricular wall is predictive of survival in different forms of cardiac amyloidosis

نویسندگان

  • Fabian aus dem Siepen
  • Rebekka Kammerer
  • Katrin A Scherer
  • Ralf Bauer
  • Stefan E Hardt
  • Evangelos Giannitsis
  • Sebastian Buss
  • Arnt V Kristen
چکیده

Background Systemic amyloidosis is a disorder characterized by extracellular deposition of different insoluble protein fibrils in various organs leading to organ dysfunction. Cardiac involvement is associated with limited survival. We aimed to use cardiac magnetic resonance imaging (CMR) to identify structural and functional alterations related to the different forms of amyloidosis, e. g. hereditary and wild-type transthyretin (TTR) amyloidosis as well as light-chain (AL) amyloidosis.

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عنوان ژورنال:

دوره 15  شماره 

صفحات  -

تاریخ انتشار 2013