A young woman with hypergammaglobulinemia, distal renal tubular acidosis and some clinical features of polymyositis.

When clinically apparent, infected aneurysms are often at an advanced stage of development or are associated with complications such as rupture. Nontreatment or delayed treatment of infected aneurysms has a poor outcome, due to fulminant sepsis or haemorrhage. Multi-detector computed tomography and magnetic resonance imaging have replaced conventional angiography as minimally invasive techniques for detection of infected aneurysms [6]. The treatment of a mycotic aneurysm is wide resection of the infected aorta and grafting followed by long term antifungal treatment. However, hospital mortality rate following surgery approaches 40% [7]. Endovascular stent-graft repair can be performed in selected cases. In our patient oral prednisolone given to treat a suspected vasculitis probably aggravated the undetected fungal infection, leading to rupture of the aneurysm. Why our patient became immunocompromised to develop disseminated Aspergillosis remains unclear.