Intestinal lymphangiectasia: a forgotten cause of chronic diarrhea.
نویسنده
چکیده
Intestinal lymphangiectasia is a rare autosomal dominant disorder or acquired condition that leads to lymph obstruction, poor chyle transport and concomitant problems. We describe the cases of two women with chronic diarrhea in whom the common signs of lymphagiectasia-hypoalbuminemia, lymphopenia and distal edema- were found. One of them also had pleural effusion and chylous ascites. The diagnosis was performed by intestinal biopsy. We herein review the histopathologic, radiographic and endoscopic features of this disorder and case reports in Mexican population.
منابع مشابه
Intestinal lymphangiectasia in a patient with autoimmune polyglandular syndrome type III.
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Primary intestinal lymphangiectasia (PIL) is a rare disease of intestinal lymphatics presenting with hypoproteinemia, bilateral lower limb edema, ascites, and protein losing enteropathy. We report a series of 4 children from Chennai, India presenting with anasarca, recurrent diarrhea, hypoproteinemia and confirmatory features of PIL on endoscopy and histopathology.
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ورودعنوان ژورنال:
- Revista de gastroenterologia de Mexico
دوره 71 1 شماره
صفحات -
تاریخ انتشار 2006