Parry-romberg syndrome: about a case
نویسندگان
چکیده
A six-year-old girl presented with skin lesions on the left cheek at 5 years of age. On examination diffuse sclerosis on the left cheek was noted, hypoplasia of left half of the face and deviation of mouth and lips to left side were noted. Investigations show normal blood counts and rheumatoid factor and antinuclear antibody were negative. CT scan of brain was normal. Fundus examination revealed a grade 2 hyalitis. Parry-romberg syndrome (PRS), also known as "progressive facial hemiatrophy" is a rare degenerative condition of the face. It is characterized by progressive but selflimiting unilateral wasting of facial skin, subcutaneous fat, muscle and occasionally bone. It can be associated with various ophthalmic and neurologic complications.
منابع مشابه
Case report of progressive facial hemiatrophy
Introduction: Progressive facial hemiatrophy (Parry-Romberg syndrome) is a rare disease ‎always with neurological symptoms such as migraine and epilepsy. Parry-Romberg syndrome ‎is determined with progressive slow hemiatrophy of skin and soft tissue structures in face and ‎frequently in left face. Disease is more common in females. The objective of this paper is to ‎present a ca...
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