Constriction band sequence along with associated malformations

Amniotic Band Sequence (ABS) also known as Amniotic Deformity, adhesion, and Mutilation (ADAM) complex or Congenital Constriction Band Syndrome (CCBS) had variety of presentation and is cause of disfigurement and disability in the newborn. This retrospective study was conducted in department of Plastic and Reconstructive Surgery, Liaquat University Hospital Jamshoro, Sindh Pakistan to determine presentation of constriction band syndrome and its association with other congenital anomalies seen at our institution. Ten patients with constriction band syndrome were included in the study. All were admitted through the outpatient department. The site and extent of each constricting ring and related anomalies were recorded. Surgery was performed. The most common associated anomalies were syndactyly, acrosyndactyly, hypo plastic phalanges, lymph edema and Talipes Equino Varus. Such type of study in our population is conducted for the first time which shows that constriction band syndrome is also not uncommon in our setup and successful surgical repair is also possible. Further research is also required in order to diagnose this in uterus, intra uterine lysis/ surgical intervention and possible causative factors needs elaboration.