Lower Extremity Fibro-Adipose Vascular Anomaly (FAVA): A New Case of a Newly Delineated Disorder.

نویسندگان

  • Israel Fernandez-Pineda
  • David Marcilla
  • Francisco Javier Downey-Carmona
  • Sebastian Roldan
  • Lucia Ortega-Laureano
  • Jose Bernabeu-Wittel
چکیده

The acronym FAVA (Fibro-Adipose Vascular Anomaly) has been recently given to a distinct vascular entity that is characterized by fibrofatty infiltration of muscle, unusual phlebectasia with pain, and contracture of the affected extremity. We report a new case of FAVA in a 10-year-old girl with pain in her right lower leg and equinus contracture. As in our case, FAVA typically presents in young females with calf involvement and limited ankle dorsiflexion with local pain. FAVA should be considered as a differential diagnosis when evaluating vascular anomalies in the lower extremities.

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عنوان ژورنال:
  • Annals of vascular diseases

دوره 7 3  شماره 

صفحات  -

تاریخ انتشار 2014