A 25 Year-Old Male with Cerebellar Mass: Lhermitte-Duclos Disease
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چکیده
We report a rare case of dysplastic cerebellar gangliocytoma also called as Lhermitte-Duclos Disease located in the cerebellum in a young male without any neurological signs. Morphologically dysplastic neurons and immunohistochemical staining with neuronal and glial markers was all diagnostic on pathology. Also a non-enhancing cerebellar hemispheric mass with a striated pattern of hyper-, and isointensity on T2-weighted images is classical findings on brain MRI. MRI findings of the lesion is
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Lhermitte – Duclos Disease in a Young Adult: Rare Entity
Lhermitte - Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar lesion which share features of both malformation and neoplasm. The usual presentation is of raised intracranial pressure along with cerebellar signs. We report a case of 23 year male who presented with headache & diplopia. MRI was suggestive of the diagnosis. Subtotal excision of th...
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Lhermitte Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar neoplasm. It usually presents with raised intracranial pressure along with cerebellar signs. We report a rare case of Lhermitte Duclos disease of a 20 years male who presented with signs & symptoms of raised intracranial tension. CT features were suggestive of Lhermitte-Duclos disease. Su...
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Lhermitte-Duclos disease, also known as dysplastic cerebellar gangliocytoma, was first diagnosed by doctors Lhermitte and Duclos in 1920. In subsequent years, the disease was described by many researchers: Bielschowsky and Simons in 1930, Christensen in 1937, Duncan and Snodgrass in 1943, Ambler in 1969, and Padber in 1991. Each of the authors referred to this disease in a different way: diffus...
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