Neurogenic scapuloperoneal syndrome in childhood.
نویسندگان
چکیده
Two brothers presented with a slowly progressive scapuloperoneal syndrome starting in early childhood. Initially there were myopathic EMG changes, but these changed to those of denervation. Neuromuscular biopsies at an interval of five years confirmed the neurogenic character of the muscle atrophy.
منابع مشابه
Adult onset scapuloperoneal myopathy: diagnostic value of nerve morphometry and multiple muscle biopsies.
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عنوان ژورنال:
- Journal of neurology, neurosurgery, and psychiatry
دوره 43 10 شماره
صفحات -
تاریخ انتشار 1980