MR imaging of Lhermitte-Duclos disease: a case report.

نویسندگان

  • R R Smith
  • R I Grossman
  • H I Goldberg
  • D B Hackney
  • L T Bilaniuk
  • R A Zimmerman
چکیده

Since 1920, when Lhermitte and Duclos first described a tumorlike abnormality of the cerebellum, which has come to bear their name, there has been an increasing number of reports of this rare entity [1-10]. Most cases have not had radiographic correlation , but there are several reported cases in which CT was part of the pretreatment evaluation [2-7], and one case was demonstrated on low-field MR imaging [6, 7]. We report a biopsy proved case of Lhermitte-Duclos disease imaged by CT and high-field MR imaging.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Lhermitte – Duclos Disease in a Young Adult: Rare Entity

Lhermitte - Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar lesion which share features of both malformation and neoplasm. The usual presentation is of raised intracranial pressure along with cerebellar signs. We report a case of 23 year male who presented with headache & diplopia. MRI was suggestive of the diagnosis. Subtotal excision of th...

متن کامل

Adult medulloblastoma mimicking Lhermitte-Duclos disease: can diffusion weighted imaging help?

Lhermitte-Duclos disease, also known as dysplastic cerebellar gangliocytoma, is a rare cerebellar benign tumor with characteristic appearance of thickened cerebellar folia giving a laminated or striated appearance, quite diagnostic of the condition. We had seen a patient with medulloblastoma with imaging findings suspicious for thickened cerebellar folia reminiscent of Lhermitte-Duclos disease....

متن کامل

Atypical MR appearance of Lhermitte-Duclos disease with contrast enhancement.

A case of surgically confirmed Lhermitte-Duclos disease demonstrated contrast enhancement on MR. Histologic examination verified corresponding increased vascularity in the molecular layer and adjacent leptomeninges.

متن کامل

Dysphagia and Neck Swelling in a Case of Undiagnosed Lhermitte-Duclos Disease and Cowden Syndrome

We report a case of a 37-year-old woman presenting with dysphagia and thyroid masses who was subsequently diagnosed with Lhermitte-Duclos disease (LDD) based on MRI scan and histopathology. Additional imaging subsequently revealed the presence of thyroid nodules and bilateral breast cancers. Genetic testing later confirmed the diagnosis of Cowden syndrome. This case illustrates the importance o...

متن کامل

Association of Lhermitte-Duclos and Cowden disease: report of a new case and review of the literature.

Lhermitte-Duclos disease is a rare entity, and its pathological features are unique. Pathological findings are characteristic of the disease, with global hypertrophy of the cerebellum, coarse gyri, and the typical "inverted cortex" pattern. Several associated lesions were noted in many patients with Lhermitte-Duclos disease. It is only recently that an association between Lhermitte-Duclos disea...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • AJNR. American journal of neuroradiology

دوره 10 1  شماره 

صفحات  -

تاریخ انتشار 1989