Call for an international survey on therapeutic lavage for pulmonary alveolar proteinosis.
نویسنده
چکیده
Pulmonary alveolar proteinosis (PAP) is a syndrome characterised by accumulation of proteinaceous, periodic acidSchiff positive material within airspaces due to disruption of surfactant homeostasis [1]. In 95% of cases, PAP is associated with increased serum levels of auto-antibodies neutralising granulocyte-macrophage colony-stimulating factor and, therefore, this form is referred to as ‘‘auto-immune PAP’’ [2].
منابع مشابه
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ورودعنوان ژورنال:
- The European respiratory journal
دوره 39 4 شماره
صفحات -
تاریخ انتشار 2012