Linear atrophoderma of Moulin located on the face
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چکیده
Linear atrophoderma of Moulin (LAM) is a dermatosis characterized by hyperpigmented and depressed band-like lesions localized along the Blaschko lines. This dermatosis was described for the first time by Moulin et al. in five patients with similar characteristics in 1992 and referred to atrophoderma of Moulin, with referrance to the first publication [1,2]. Major characteristics of LAM are being unilateral, following the Blaschko lines, long remain unchanged, onset in the childhood or adolescent period and lack of the induration. The lesions indicate progression over the first few months, then after having a linear atrophic state they stop the progression, limit themselves and become persistent [3]. Despite clinically atrophic appearance of the lesions, elastic and collagen fibers are usually normal in histopathological examination [2]. Etiology of LAM is unknown. Its localization matching the Blaschko lines is thought to be a reflection of mosaicism, which is believed to develop due to a somatic mutation occurring during early embryogenesis [4,5].
منابع مشابه
Linear atrophoderma of Moulin: a case report and review of the literature
Linear atrophoderma of Moulin (LAM) is a rare dermatosis in childhood and early adolescence. The exact etiology of LAM is still obscure. Several treatment modalities were reported but none was consistently successful. We report a case of LAM in which a favorable outcome was obtained with topical calcipotriol. The relevant literature is also reviewed.
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Linear atrophoderma of Moulin (LAM) is an acquired skin condition that manifests in early childhood and adolescence. It likely represents a form of cutaneous mosaicism that presents with linear, hyperpigmented and atrophic lesions appearing on the trunk and limbs. Its clinical appearance varies and may closely resemble that of atrophoderma of Pasini and Pierini (APP) and linear scleroderma. LAM...
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the pretibial areas. Erythema ab igne. Arch Dermatol 1990; 126: 386 ± 387. 4. Meffert JJ, Davis BM. Furniture-induced erythema ab igne. J Am Acad Dermatol 1996; 34: 516 ± 517. 5. Butler ML. Erythema ab igne, a sign of pancreatic disease. Am J Gastroenterol 1977; 67: 77 ± 79. 6. Ashby M. Erythema ab igne in cancer patients. J R Soc Med 1985; 78: 925 ± 927. 7. Arrington JH 3rd, Lockman DS. Therma...
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