Rosai-Dorfman disease presenting as large pigmented indurated plaques.
نویسندگان
چکیده
Yuichiro Tsunemi, Hironobu Ihn, Yuka Shimada, Kazuhiko Takehara, Motomu Manabe and Kunihiko Tamaki Department of Dermatology, Faculty of Medicine, University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo 113-8655, Department of Dermatology, Faculty of Medicine, Kanazawa University and Department of Dermatology, Akita University School of Medicine, Japan. E-mail: [email protected] Accepted August 27, 2002.
منابع مشابه
Histological variability and the importance of clinicopathological correlation in cutaneous Rosai-Dorfman disease*
Rosai-Dorfman disease is a benign histiocytic proliferative disorder of unknown etiology. The disease mainly affects lymph node tissue, although it is rarely confined to the skin. Here, we describe a 53-year-old woman with purely cutaneous Rosai-Dorfman disease. The patient presented with a large pigmented plaque on her left leg, and sparse erythematous papules on her face and arms. A complete ...
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Rosai-Dorfman disease is a rare condition of marrow hematopoietic stem-cell origin. Patients can show extranodal involvement as well as lymphatic involvement, but only about 5% of extranodal cases involve intracranial lesions. A 53-year-old male was admitted to our hospital with bilateral cervical lymphadenopathy. Intracranial tumors and bone lesions were also detected. Cervical lymph node biop...
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H syndrome is an autosomal recessive genodermatosis with reports dating back to the last decade. This syndrome is caused by mutations in the SCL29A3 gene. The clinical characteristics of this syndrome consist of dermatological manifestations, including hyperpigmented, hypertrichotic, and indurated patches and plaques. It affects various systems by causing heart anomalies, hepatosplenomegaly, hy...
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UNLABELLED Rosai-Dorfman Syndrome (RDD) is a rare, benign, self-limiting disorder which is characterized by the non-malignant proliferation of distinctive histiocytic cell within lymphatic system. RDD has been described as a dynamic entity in the spectrum of histiocytosis with non-Langerhans cell histiocytosis at one end and Langerhans cell histiocytosis at the other. The exact etiology of this...
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ورودعنوان ژورنال:
- Acta dermato-venereologica
دوره 83 1 شماره
صفحات -
تاریخ انتشار 2003