Sturge-Weber Syndrome Complicating with Ipsilateral Hemangioma-liked Nasal Polyps
نویسندگان
چکیده
Sturge-Weber syndrome (SWS), also known as encephalotrigeminal angiomatosis, was reported by Schirmer, Sturge and Weber in succession in mid-19th century. And it is a neurocutaneous disease classically presenting with a facial portwine stain in the ophthalmic distribution of the trigeminal nerve, glaucoma and vascular eye abnormalities, and an ipsilateral occipital leptomeningeal angioma. It is possible to observe nose and sinus involvement in SWS [1]. And there already have been some cases about SWS accompanying with chronic rhinosinusitis [2], but to our knowledge, there are still no cases describing SWS combining with ipsilateral chronic rhinosinusitis and unusual nasal polyps. Here, we report a case of SWS which incorporated with ipsilateral chronic rhinosinusitis and nasal polyps-more precisely hemangioma-liked nasal polyps.
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Background: Sturge-Weber syndrome is one of the rare neurocutaneous disorders with frequency of approximately 1 per 50,000. Sturge-Weber syndrome consists of a constellation of symptoms and signs including a facial nevus (port wine stain), seizure and hemiparesis. In many cases it may associate with mental retardation. Case presentation: A 7- year old girl with mental retardation and a large fa...
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