Kidney transplantation in infantile myofibromatosis and fibromuscular dysplasia: a case report
نویسندگان
چکیده
INTRODUCTION We report what we believe to be the first case of a child affected by two rare vascular diseases complicated by kidney failure and successfully treated by kidney transplantation. CASE PRESENTATION A 3-year-old Caucasian girl with fibromuscular dysplasia and infantile myofibromatosis presented with arterial hypertension and renal failure. She received a deceased donor kidney transplantation distal to an iliac graft. The technical peculiarities of this transplantation are described, as well as her favorable long-term outcome. CONCLUSION Kidney transplantation may be considered in a patient with vascular diseases and a history of iliac surgery.
منابع مشابه
Successful transplant of a kidney with fibromuscular dysplasia having higher glomerular filtration rate than the contralateral kidney.
Fibromuscular dysplasia is the second-most commonly encountered anatomic abnormality in potential renal donors. Normotensive patients with medial fibroplasia and low-grade lesions have been used as renal donors. However, no studies have reported the optimal choice of a kidney for donation where the kidney with fibromuscular dysplasia had a larger volume and a higher glomerular filtration rate t...
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Dear Editor, In the case report by Sun and associates, follow-up of 1 year is not adequate time to comment on the outcome and make recommendations because most complications occur long term.1 In a previous case, the donor developed fibromuscular dysplasia 8 years after donation.2 Rapid progression of native renal artery fibromuscular dysplasia has been reported 1 year after kidney donation.3 In...
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Background: Renal artery stenosis, which is defined as narrowing of one or both renal arteries or their branches, is one of the most common causes of secondary hypertension. The majority of renal vascular lesions show either fibromuscular dysplasia or atherosclerosis. Fibromuscular dysplasia is a common cause of renovascular hypertension in younger patients, and 90% of patients are young wome...
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BACKGROUND Infantile myofibromatosis is a rare mesenchymal disorder of infancy that can extensively involve the viscera including the gastrointestinal tract. CASE PRESENTATION In this report, an exceptional case of infantile myofibromatosis is described in which rectal prolapse and sigmoid colo-colonic intussusception were the initial presentations of colorectal involvement in a 2-month-old p...
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