AL amyloidosis in a young adult: remission with autologous stem cell transplantation.

نویسندگان

  • Ricardo Prado Golmia
  • Isabel Clapis Bello
  • Eliane Rosseto
  • João Carlos Campos Guerra
  • Cristóvão Mangueira
  • Morton Aaron Scheinberg
چکیده

Autologous stem cell transplant is one of the therapies employed in the treatment of primary amyloidosis or AL. The authors report on a 46-year-old patient with bilateral periorbital hematomas, macroglossia who presented, during the investigation, IgG-Kappa paraprotein in serum. The diagnosis of primary amyloidosis or AL was confirmed and the treatment proposed consisted of high-dose melphalan as conditioning regimen before autologous stem cell transplant, which determined complete remission of the disease, along with the disappearance of clinical signs and absence of the monoclonal component.

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عنوان ژورنال:
  • Revista brasileira de reumatologia

دوره 50 5  شماره 

صفحات  -

تاریخ انتشار 2010